Zempilo, Diseases and nemibandela
Ukukhubazeka uneDuchenne-Erb: Oonobangela kunye Treatment
uphuhliso amayeza ngokuqhubekayo. Yonke imihla, izazinzulu ceba amachiza amatsha zinika iindlela eziphuculweyo yokuqhuba imisebenzi. Nangona kukho inkqubela ebonakalayo kule ndawo, ingxaki ukuzalwa ngokuzenzakalisa esasebenza. Le ngozi inkulu uvelisa hayi ngezifo kunye neziphumo zawo. Umzekelo obalaseleyo disorder luvo, apho umntwana unako ukufumana ngexesha delivery, a plexus kukwenzakala brachial. Ukuba utshintsho iqatshelwe isakhiwo amathambo wesibeleko, ukukhubazeka kwafunyaniswa ukuba uneDuchenne-Erb. Iimbangi ezingundoqo izifo kunye neendlela zonyango iza kuxoxwa ngezantsi.
Inkcazelo emfutshane ye sifo
isifo engabalulekanga luvo ukuvela ngenxa umonakalo onedumbe brachial plexus kuthiwa uneDuchenne-Erb. Oku kudla kwakhokelwa yokwenzakala ngokuzalwa. Ngoko ke, lo ngezifo idla ngokuba ekukhubazekeni yokubelekisa. Noko ke, le unobangela kuphela kule meko.
Lubonakala yi kubuthathaka kwezihlunu kwi yesiqephu eliphezulu, luthintelo ukushukumiseka kwi emagxeni kunye uyibhekise amalungu. Kwakhona kukwaphula uvakalelo kunokwenzeka, kodwa zigcinwe iibhrashi motility. Yokubelekisa palsy uneDuchenne-Erb ukuba akunakwenzeka ukuba boyise, ukuba sisebenzisa inkqubo jikelele unyango. Unyango usoloko ekhethiweyo ngamnye. Esinye isigulane emva kokuba ugqirha yoviwo imisela amayeza eyanele, abanye - ukuyifundisa. Kwiimeko ezinzima kakhulu zifuna uqhaqho. Sase- recovery kuxhomekeke ubungqongqo ngezifo kunye nokuphelela ngonyango.
imvelaphi ezeMbali ezinye manani
Ukukhubazeka uneDuchenne-Erb igama imbeko neurologists ezimbini. Baya kuqala ukuchaza ngokweenkcukacha umyalezo kwesifo kunye nekliniki. Ugqirha French G. Duchesne iminyaka emininzi ukufunda imo izigulane abatsha emva kokuzalwa enzima. Ngowe-1872, washwankathela ingcaciso efunyenweyo kwaye wanikela inkcazelo eneenkcukacha iimpawu ukukhubazeka kwiintsana. Eyayingqalene isifundo sifo ababandakanyekayo omnye ugqirha saseJamani W. Erb. Wakwazi ukuchaza umfanekiso yokwakheka yophuhliso izifo Pathogenesis yale nkqubo abadala.
Ngokutsho manani, ukukhubazeka yokubelekisa ka uneDuchenne-Erb yeyela kudidi ezimbi ezinqabileyo. Okwangoku, isifo eso kuqinisekiswa zonke iintsana senkulungwane. Nangona ukuphuculwa rhoqo kobuchule yokubelekisa, esi sifo luhlala ingxaki ngokwemixholo zezonyango namhlanje.
Izinto ezibangela ukukhubazeka kwamalungu kubelekwa
Ukukhubazeka uneDuchenne-Erb sosana kuphuhliswa sizoku lwisana plexus ebuhlungu brachial. Xa inkqubo kokuziswa kwekhithi, obstetrician kufuneka enze iintshukumo ezahlukeneyo ukunceda umntwana azalwe. Kufuneka kuqatshelwe ukuba wenziwa amanyathelo kuphela kwiimeko ezingxamisekileyo. Ngexesha lezi zazo zinokwenzeka:
- kuhlukunyezwa nemisipha ileli ;
- yade le plexus brachial, i-luvo uthatha ikhefu;
- ukopha engephi kummandla ochaphazelekayo.
Ukuba umbungu mkhulu kakhulu, kwaye parameters zayo musa ukuthelekisa ubungakanani lomsele wokuzalwa, umngcipheko umonakalo egxalabeni ukunyuka ezidityanelweyo izihlandlo eziliqela. Ukuze uncede umntwana wakho azalwe, ababelekisi banyanzeleka ukuba basebenzise izixhobo ezikhethekileyo. Xa iintshukumo elibukhali kuyasa Imicu brachial plexus luvo.
Izinto ezibangela ukukhubazeka kwamalungu abadala
Xa abantwana abadala kunye nabantu abadala, uphuhliso ngezifo lidla ezinxulumene ukumelana nonxunguphalo. Phakathi kwezi umonakalo ziquka:
- nengalo ibambelele;
- ukulimala entanyeni;
- plexus ukonzakala brachial kummandla;
- elula.
Ngamanye amaxesha brachial plexus nenxeba ngenxa yengozi yemoto. Ezinqabe kakhulu Erb-uneDuchenne zizihlunu abadala evukayo sisilonda esidumbileyoesingaphakathi eziyityhefu okanye esosulelayo. Ukuphuhliswa kwenkqubo zophendlo lwezifo ezinokubangelwa usuleleko TB aphuma ngendlela enzima, umkhuhlane kunye nesifo seengcongconi.
Ziziphi iimpawu zibonisa izifo?
Ngophuhliso ekuthiwa ekukhubazekeni iyathamba waphawula ilahleko umsebenzi eziliqela izihlunu (izo-, deltoid, igxalaba). Ubuzaza iimpawu umonakalo kuxhomekeke kuhlobo imicu, ukungaqheleki ukubetha Uhanjiso.
kubelekwa ezininzi palsy uneDuchenne-Erb bubonakala ngemihla yokuqala yobomi. Umntwana liba ngokugqith 'emgceni yaye rhoqo ekhala. Unobangela sifo intlungu kakhulu kwi imilenze. Kwakhona kwi ukwenzakala brachial plexus asenokubonisa ukuba mpawu zilandelayo:
- njalo kancinci wavula ngesandla kwi engqinibeni;
- yehle kwezihlunu;
- ekuncipheni umoya;
- grip isandla inqindi kunye ubhontsi;
- isikhumba sakuba.
Nangona isilela umsebenzi esandleni isibetho, abantwana badla livakale lwezithuthi eziphantsi. Noko ke, ukuba usana walala phantsi entendeni kwesebe bachaphazelekayo kancinane Alenga.
Izigaba inkqubo flow zophendlo lwezifo
Ukukhubazeka uneDuchenne-Erb yaphuhliswa ngokwamanqanaba eziliqela.
Isigaba Acute ithatha iiyure eziliqela ukuya kwiintsuku 2-3. Ngeli xesha, kukho ukuhla umsebenzi wezandla, ubunzima ngokugoba ingalo uyibhekise kwenkqubo.
Kwandule ke ukubakho kwisigaba recovery. Ngonyango olufanelekileyo yamaziko sasilungiswa imisebenzi elahlekileyo kungathatha iminyaka emininzi. Ngenxa yoko, umonakalo luvo ifayibha le nokudumba shwaka, kunye nokuhamba kwegazi IbuyiselweName ngokupheleleyo.
Emva koko kuza kwenzeka neziphumo intsalela obuluqilima nobuhlala ixesha elide. Ngoko ke, kubalulekile ngexesha recovery bamatasa kulo unyango. Eqongeni, naziphi na iziphumo ntsalela zongenelelo zonyango lingama ayisasebenzi. Kwesebe nomonde ochaphazelekayo ngokuthe hypertrophy, ngelixa yokulimala ibonakala akuqolanga. Ibe likhaba ngecala isigulane zocaphulo, enyeleni ihambisa kude kwalapho. Ekuhambeni kwexesha, ezi nguqu akhokelela esime yomqolo - zokufota.
Njani na isifo?
Imizekelo uneDuchenne-Erb uphando palsy nangoku riveting ingqalelo izazinzulu evela ehlabathini lonke. Namhlanje, Noko ke, isifo inkqubo zophendlo lwezifo akuthethi ukuba naziphi na iingxaki. Xa iimpawu zokuqala wabantwana bakhe kufuneka athumele kuzalwa ukuya kokubonisana emine kunye zamathambo. Xa izigulane abadala, unyango sifo nazo inxaxheba kwezi iingcali. Ukuze ufake isifo luvo kufuneka bafunde imbali yomguli, ukuqhuba iimviwo emzimbeni. Ngoku yisa ku uviwo eneenkcukacha equka:
- electroneuromyography;
- MRI;
- myelography computer;
- dinanometriyu;
- reovasography;
- Ultrasound iimviwo kwegxalaba.
Ngokuqhelekileyo, wabonakala engaphandle sifo ngokwaneleyo ukuqinisekisa esi sifo. ke lonke ulwazi ekufuneka wangena card yezonyango yesigulane. Ugqirha yenza inowuthi, yenza uphethwe "Erb-uneDuchenne ukukhubazeka." ICD-10 Wacebisana ikhowudi R14.0 sifo.
Noko ke, ukuba ukuchonga uhlobo umonakalo oqhuba ezi izifundo ezifunekayo. Nganye kwezi ndlela loxilongo ithwala umsebenzi othile kwaye ayikwazi ingathathelwa indawo lelinye. Ngokusekelwe kwezi ziphumo zovavanyo, ugqirha wakho angakunika unyango, ngokunjalo ukunika sase- elizayo.
unyango ngamachiza
unyango ukukhubazeka luqala ngeendlela angqingqwa. Kwisigaba etsolo akusoloko kusenzeka ukuba iqondo umonakalo imicu ngenxa nokudumba eyomeleleyo kwithishyu. Ngako oko, iinkqubo zotyando zithathwa ukuba angafaneleki.
Ziziphi amayeza zisetyenziswa ukulwa nalo ngezifo, engasentla unedumbe uneDuchenne-Erb?
- Nonsteroidal amachiza anti-ukudumba: "ibuprofen", "Amidopyrine".
- Amayeza ukuphucula kwegazi, "Pentoxifylline," "papaverine".
- amachiza Anticholinesterase eziphucula amaza luvo, "Neuromidin", "galantamine", "Neostigmine".
- Amalungiselelo ukuba kuqheleke ukutya "Aktovegin", "Meksidol" nezakhiwo vitamin.
Kunye nokuphuculwa amayeza idosi idosi kwirejimeni yesigulane iyahluka.
iinkqubo Physical therapy
Ukulwa inkqubo sifo ithetha ebizwa ngokuba yi-isikhundla unyango. Kwi kwesebe egula enyanzeliswa phezu ibhasi leyo lungasuswa kuphela ngexesha iinkqubo yococeko.
Ukuze sihlale kwemisipha ithoni ibonisa, imisebenzi efana:
- uhlikihla lo mlenze ochaphazelekayo (ukuqala ukusuka kwiveki yesibini);
- nqgo umsipha sombane ;
- ukuyifundisa ne umzimba nje;
- acupuncture;
- maqula zeparafini;
- ozokerite.
Isiphumo emihle unyango endala kunokwenzeka kuphela xa ukutshatyalaliswa kwenxenye imicu brachial plexus. Yena elinde iinyanga ngathi zaba ntathu, waza badlule ukuvavanywa kweziphumo. Ukuba ngeli xesha isigulane alibonakali intshukumo ebonakalayo engqinibeni, umbuzo malunga nokusebenza.
ukungenelela kuhlinzwa
Kakuhle eli msebenzi lifinyele ukubuyisela ingqibelelo imicu ezonakeleyo. Ziziphatha-luvo umboko zeplastiki. Okwangoku ke lo msebenzi kuphela ukuba ukunceda izigulane unesifo "ukushwabana uneDuchenne-Erb." Unyango kwenziwa kunyaka wabo wokuqala bezelwe isigulana encinane, unika iziphumo ezingcono. Olu tyando alisusi iimpawu zenkqubo yezifo. It ikuvumela ukuba ukubuyisela indlela apho inkqubela-luvo ishukuma. Koko kuboniswe unyango endala usebenzisa unyango ngokwasemzimbeni, umyalezo.
Liqikelele elizayo
Kufuneka kuqondwe ukuba unyango zobulima yokubelekisa - yinto umsebenzi elide kwaye onzima ukuba kufuneka ube nomonde. icebiso Zonke kagqirha kufuneka ilandelwe kanye ukuze ufumane iziphumo ezidibanisayo. Ezininzi iinkqubo anaba kangangeenyanga, ingakumbi kunyango ngokwasemzimbeni kunye umyalezo.
Zizihlunu ingagcina uneDuchenne-Erb: ukukhubazeka okanye recovery? Ngelishwa, ukunika impendulo ngqo lo mbuzo akwenzeki. Konke kuxhomekeke kwizinto ezifana:
- ubungqongqo wokwenzakala;
- ukufaneleka kunye nokwanela unyango;
- umnqweno ukwenza yonke ingcebiso kagqirha.
Ukuba amanxeba inxenye ye plexus brachial nga nethemba 100% recovery. Ubuncinane lithi manani. Xa olupheleleyo bodwa ithuba, ngelishwa, lincinane kakhulu.
amanyathelo othintelo
Ngaba kunokwenzeka ukuba ukuthintela ukushwabana uneDuchenne-Erb? Amafoto abantwana abaselula kwafuneka lijongane nale sifo, ngokwenene kukwenza ucinga ngalo mba.
Enyanisweni, nokuthintela izifo ilula. Oku kuthetha ngoncedo kwangaphambi, ukhetho oluchanekileyo lwe-ndlela wokuziswa. Kwanaxa nqanaba kufuneka uthathe unonophelo icebo layo karhulumente, zama ukutya ekunene kwaye wenze imidlalo siyixabise. umfazi okunempilo kungenzeka ukuba kuzala ngaphandle ezimbi. Ukongeza kukhetho yeziko lezempilo apho umama okhulelweyo ugqiba ukuba kwenzeke, kufuneka kucelwe ngenkathalo. Kufuneka sifunde ukuhlaziywa malunga obstetrician, inkqubo yokunikezelwa kule kliniki. Unako kwakhona bathethathethane abahlobo abaye sele ulawulwa ukuzama indima kamama. Ngexesha lokukhulelwa kakhulu ngqo kubalulekile ukuphulaphula ngengcebiso ugqirha, musa ngoyaba izindululo.
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