Ectodermal kunye dysplasia ezinezikhondo. kidney dysplasia

Phantsi dysplasia (Liguqulwe lithatyathwa Greek njengoko dys - ukuphika; wplasis - imfundo) ibhekisela engalunganga kwaye ukutyhefa nophuhliso naliphi na iziko. Le - igama elihlanganisayo egubungele naziphi na ukunyhashwa.

dysplasia ezinezikhondo ibhekisa izifo kwenkqubo skeletal, kwaye Eboniswe ukuba inwebu ithambo luthathelwa izihlunu ezinezikhondo. Le nkqubo deforms amathambo. Esona sizathu sokuba esi sifo imbonakalo inkqubo ithumba, eqala lo mntwana, waza emva koko iqala inkqubela. dysplasia ezinezikhondo ngesiqhelo ekwi kwabasetyhini.

isifo ukuhlelwa eziliqela. Iyunithi iqhelekileyo, ngokuxhomekeke kwinqanaba ukwanda yenkqubo yezifo:

• monoossalnaya dysplasia ezinezikhondo kuchaphazela ithambo enye kuphela;
• poliossalnaya - utshintsho kuvandlakanywa emathanjeni ezininzi (idla kwanwenwa kwelinye icala lomzimba, yaye ngokufuthi kwenzeka ebuntwaneni).

Ifomu yokuqala sifo sichaphazela ithambo cranial, intsimbi, amathambo tubular (ixesha elide) buthelezi. Okwesibini - ngaxeshanye ngaphezulu kwamashumi amahlanu ekhulwini onke amathambo amathambo.

Iingxaki eziphambili ziquka kwizaphuko rhoqo, nto leyo coalesce ngokukhawuleza, kodwa uhlobo Olomeleziweyo emathanjeni, kwakunye nee-.

dysplasia ezinezikhondo naluphi na unyango ayikwazi ukuba, ingaba iinkqubo kuphela wamathambo (yotyando curettage ithambo, osteotomy), kwaye ukuqeshwa iziyobisi kukunciphisa intlungu.

dysplasia Ectodermal kubandakanya inani elikhulu kwezifo kunye syndromes (malunga ne-100), eli leyo phambi kophuhliso engaqhelekanga avela ectoderm. Uphawu lokuqala - phambi komzimba, leyo xa luboniswa, kunye ekuhlaseleni kungakhokelela nokwaphulwa naluphi na uphuhliso lweengqondo, okanye ukufa.

Ungakhetha ezi ntlobo zilandelayo kunye neempawu zazo.

Angidroticheskaya uqala ukuzibonakalisa kwiintsana, inkwenkwe kuze kuqhube ebomini. Ezona mpawu ziphambili zezi:

• izifo zofuzo;
• deformation enamandla amazinyo;
• ubukho ukudodobala amanxeba;
• yoma mucosal (umqala, umlomo, impumlo);
• imbonakalo yangaphandle kuyafana izigulane umntwana ukuba negcushuwa naso.

unyango lingaze kunikwa. Ezingavumelekanga: leeholide kumazwe emazantsi, umsebenzi izityalo ezishushu imichiza.

Gidroticheskaya ekzodermalnaya dysplasia luphawulwa utshintsho ezintendeni, ekuncothukeni kweentende zeenyawo, uphuhliso iinwele. Njengoko unyango esuke vitamin "A" ngaphandle nangaphakathi, cream ukuthamba kunye keratolytics. Ukongeza koku, sebenzisa: enzymatic kuthetha Methyluracilum, steroid, zinc, acid kunye biostimulants.

dysplasia sezintso na iintlobo ezininzi ezahlukeneyo:

• obubonakala morphological (esinganyangekiyo kunye ezilula);
• Kwasendaweni (cortico-medullary, medullary kunye cortical);
• ukwanda - iyonke, segmental, focal).

Esona sizathu sokuba esi sifo zizinto ufuzo kunye nempembelelo eteratogenic lwangaphakathi nolwangaphandle kwi mbungu. Ngoko ke, ngenxa zesifo malformations iziphene, leyo, kungakhathaliseki uhlobo, kukhokelela ekuncipheni ubukhulu kidney, uphuhliso zikhohlakeleyo parenchyma, unciphiso ebalulekileyo imisebenzi yayo.

Unyango lwesi sifo yi amatyala ibonisa kwaye rhoqo xa kukho inkomba abohlukeneyo welungu.

Ngokubanzi, dysplasia iquka iqela kwezifo ebandakanya uphuhliso okungaqhelekanga yeziko okanye inkqubo yonke. Njengoko umthetho, i ephambili ebangela - ufuzo kunye bekhubazekile.

Unyango ibonisa, okanye iziphakamiso ngenxa yotyando ilungu okanye ithambo.