ZempiloDiseases and nemibandela

Proteus Syndrome: Iimpawu kunye Indlela Treatment

Ukuza kuthi ga ngoku, Proteus syndrome uthathwa iseliswelekile kakhulu sisifo yemizila yemfuza, nto leyo sikhatshwa yokukhula nemvelo le amathambo, izihlunu zomzimba nokuqina. Ngelishwa, isifo kwaye afumane unyango lwesifo enjalo - inkqubo nzima kakhulu kwaye akusoloko kusenzeka.

yesilungu, kuyaziwa kuphela ukuba Proteus syndrome sisifo sofuzo kwaye unxulunyaniswa kuguquka zofuzo. Nangona kunjalo, indlela ukwenzela iziganeko ezi nguqu nangoku ayiqondwa ngokupheleleyo.

Proteus Syndrome: A incinane

Kuba okokuqala sifo kuchazwa 1979. Naso xa Maykl Koen esaqala 200 ukuqhambuka kwesi sifo ehlabathini ihlabathi. Yaba lo ofundileyo wamnika igama sifo. Proteus - uthixo ulwandle kwiintsomi zamaGrike. Kwaye, ngokwe iintsomi zamandulo, nkulunkulu akwazi ukutshintsha imilo kunye nobukhulu umzimba wakhe.

Proteus Syndrome: Iimpawu

Eneneni, esi sifo kufuneka sikhatshwe ezahlukeneyo iinguqu kunye nokuphazamiseka. Ngokuqhelekileyo, abantwana abagulayo bazalwa eqhelekileyo, kwaye kuphela iminyaka zotshintsho aqale. Okubangel 'umdla kukuba, kwimeko nganye, iimpawu inokuba nomahluko. Kwezinye izigulane, yokugula ugqitywa ngengozi, ekubeni akukho zimpawu zangaphandle alikho. Abanye izigulane, phezu koko, phantse bonke ubomi bakhe ukubandezeleka ebubini.

Njengoko sele kukhankanyiwe, Proteus syndrome (afanekiselwa) sikhatshwe ukukhula yethishyu - kunokuba abe nemisipha, ithambo, ulusu, nkovu kunye nempahla yegazi, okunamafutha kwithishyu. Neziqu angavela phantse naphi na. Umzekelo, kukho ukwanda ubungakanani intloko omzimba, utshintsho kwimo yabo yesiqhelo.

Kufuneka kuqatshelwe ukuba ukuba ubomi babantu lifinyele. Zibe lula ziingxaki kunye nenkqubo yokujikeleza (Embolism, deep vein thrombosis), kwakunye nomhlaza kunye goiter.

Ngokwawo, Proteus syndrome akubangeli ukulibaziseka yophuhliso. Kodwa ngenxa yokuba imithana olumandla kwithishyu kusenokuba izibhaxu yesibini luvo.

Proteus Syndrome and ngonyango

Kuba isiqalo kubalulekile ukuphawula ukuba isigulo kwangethuba kubaluleke kakhulu. I ngaphambili esi sifo kuchongwa, ithuba elingcono lo mntwana ubomi obutofotofo ngakumbi. Njengazo zonke izifo sofuzo kwaye enaso, ingxaki ayisiso isisombululo single - akunakwenzeka ukuba balahle onaso. Kodwa iindlela amayeza mihla iya kunceda ulwe iimpawu eziphambili.

Ngokomzekelo, xa ukukhula esiqwini ithambo, zokufota, ubude ezahlukeneyo kwamalungu mhlawumbi unxibe izixhobo ezikhethekileyo wamathambo ukunceda ukuhlangabezana nale ngxaki. Ukuba isifo lu dityanisiwe ezingaqhelekanga kwinkqubo yokujikeleza okanye ithumba, isigulane kufuneka ahlale phantsi kweliso lomgadi gqirha.

Ngokufuthi zisetyenziswa kunye nonyango yotyando. Ngokomzekelo, esebenzisa umsebenzi Ungalungisa niyagrenyana, yayinqamlela amathambo iminwe, ukuba umntu unako ukusebenzisa izandla zombini. Ngamanye amaxesha ufuna ukulungisa amathambo kunye zomzimba nokuqina ye isifuba, ukuze bawubuyise emikhuhlaneni uphefumla iingxaki nokuginya.

Nakowuphi na umzekelo, oku sifo kufuna ingqalelo kunye nokhathalelo njalo. Indlela kuphela ukuba abambe ubomi kunye nokuphucula ubulunga bayo.

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