Lefgrena syndrome: Oonobangela, iimpawu yiklinikhi, unyango, uthintelo

izifo Systemic zisoloko imfihlelo ehlabathini zonyango. Omnye sarcoidosis, nto leyo eye akagwetyelwa kwaye eboniswe ngohlobo ukudumba zomzimba nokuqina amasebe awohlukeneyo kunye nezihlunu lokusekwa granulomas lo umyalezo. Lefgrena syndrome - a esikhethekileyo sarcoidosis ezichaphazela eluswini, iindawo nkovu intrasternal namalungu.

oonobangela

I-Pathogenesis luphuhliso impendulo sokuhlasela. Le iingozi inkqubo yomzimba yokuzikhusela, yaye iiseli ezimhlophe zegazi kuqala ukubetha baphilileyo iiseli emiphungeni, amalungu kunye nesikhumba.

Lefgrena syndrome ngokufuthi ikhula amabhinqa aselula (iminyaka 20-35). Abantwana ludla musa begula. Lefgrena syndrome iqala wayibona, uze emva koko ngokuthe ngcembe wabonakala lwezonyango ngokunokwabo uthathe indawo. Amaxesha amaninzi, kukho izifundo ezifanelekileyo esi sifo.

Ngaphandle theory wentsholongwane egazini kunye iintsholongwane yophuhliso sarcoidosis, kukho kwakhona nenkolelo ukuba esi sifo senzeka abantu ixesha elide wadibana imichiza aziphethe ngayo mveliso. Kufuneka singalahlekani, kunye into njengelifa. Kungenxa yoko le nto sarcoidosis polyetiological sisifo samathambo.

kubonakaliswa clinical

Lefgrena sifo ngo sarcoidosis ubonisa polisimptomno. obubonakala zonyango ziqala wayibona. Umntu uba erythema nodosum emzimbeni, oko has ukuthambekela ukusasaza kwiziphelo, emva, isisu kunye nentamo. Nodes babe seqanda, ubukhulu zabo ukufikelela ukuya ngokweesentimitha 6. Kufuneka kuqatshelwe ukuba endaweni yokuba kusekwe erythema akuyonto necrosis.

Nokubonakaliswa ephambili kuthathwa ukuba ngokoyiswa inyumoniya kunye tracheal namadlala. Oku kubonisa ingozi enkulu ukuba umguli:

• a khohlo;
• wambi lobushushu emzimbeni inyusiwe;
• yonakala zezempilo;
• kukho nto yokubila ebusuku;
• lehla izinga ebuthongweni;
• komzimba kwenzeka;
• ukuba umntu uba nexhala.

Kamva Lefgrena syndrome luphawulwa izitshanguba namalungu. Baba edematous buhlungu nezokunyuka kuguga. Nangengqwalasela enkulu, umntu phawula ekweneni nodes nkovu entanyeni kunye amakhwapha.

Indlela ukuxilonga?

Lefgrena syndrome lusekiwe ngokusekelwe uxilongo elebhu kunye noviwo lwe therapist yesigulane. Erythema nodosum linendima ebalulekileyo zokufumanis olu hlobo sarcoidosis. Noko ke, ugqirha kufuneka zingahlukaniswa isifo sephepha okanye izifo dermatovenereological.

iimvavanyo zegazi Laboratory iya kubonisa:

• ukwanda ku ESR;
• leukocytosis;
• imbonakalo gamma globulin.

Kwi X-ray umfanekiso inokubonwa iindawo nkovu iimpawu ezandisiweyo, kwakunye iidipozithi ezinezikhondo. Oku kunceda ukuqinisekisa kwimeko yesifo semiphunga.

Okwanamhlanje kuchazwe kule fom ifuna ukuba bronchoscopy kunye biopsy. Xa isifundo esiqwini wemiphunga akakwazi ukubona isakhiwo mpawu histological of sarcoidosis: ubhaqa indlela iziqalelo granulomas epithelioid.

Abantu abane kunye iingxaki sifo

Ngabanye kwemali Lefgrena syndrome. Koda kube nini kwaye yintoni na uqikelelo ukuze baphendule kuphela kwemibandela ethile. Yinto eyaziwayo ukuba omdala umntu, ukuba abantu abane amahlwempu. Ukuba ngaba isicelo ngexesha ukubona ugqirha, syndrome lilibaziseka ngenyanga yaye uye uncediswa iingxaki:

• kokuphazamiseka inyumoniya;
• insufficiency zemigudu;
• uphuhliso 'intliziyo pulmonary ";
• emphysema;
• a flora virus.

ukusilela yokuphefumla emva kokuphazamiseka inyumoniya. imeko yomguli kuxhaphaka yokwanda emiphungeni baqale indawo kwizicwili, le nkqubo ukuze bayeke ngokuzenzekelayo emva kweminyaka 1-2.

Ngokuthe ngcembe, intliziyo iqala ukunyusa ngenxa yokunqongophala kwe-oksijini egazini. Kodwa asifanele ngoyaba isibheno uncedo lonyango, kuba ngoku Lefgrena syndrome ngcono.

unyango

Ngelishwa, Medco awanako ukunyanga sarcoidosis ngokupheleleyo, ekubeni umyalezo wayo ayaziwa ngokupheleleyo. Kodwa oogqirha ukumisela unyango olukhethekileyo uyakwazi ukumisa inkqubo yophuhliso, iliso Lefgrena syndrome. Unyango luqala kuyo amachiza steroidal anti-ukudumba ukuba nezifo eliphantsi. Kwakhona emiselweyo vitamin izakhiwo, antioxidants, immunosuppressants.

Ikhosi ye unyango ihlala i-avareji yeenyanga 8. Konke kuxhomekeke iimpawu ngamnye kwamajoni omzimba. Lomqulu umyalelo medical ngetsheki-up for igqirha pulmunologom abagulayo, ngokuyinene kuthatha iminyaka emi-5.

Yintoni ekuthinteleni?

Ukuthintela uphuhliso sarcoidosis, kufuneka kuqala kuyinyamekela indlela yabo yokuphila. Ukutya kufuneka kube elungeleleneyo, eziquka amafutha, iiprotheni, carbohydrate an ratio ngokupheleleyo.

Abantu kubuphepha sarcoidosis, kufuneka uyeke ukutshaya, kumfowunelwa imichiza ndlongondlongo.