ZempiloDiseases and nemibandela

UEnoki ukuba izifo: Pathogenesis, iimpawu, ozibonayo

Sophele vasculitis (uEnoki-Schonlein isifo purpura) bobabo diatheses ezifunyenwe yabangela ukwanda kuluncedo xa permeability beendonga isitya. Kukho iintlobo ezininzi ukubonakaliswa kwayo. Igama "uEnoki-Schönlein 'ukuya kwamanye amazwe. Igama elithi "vasculitis gemorrragichesky" lisetyenziswa kuphela amayeza lwasekhaya ukususela ngowe-1959.

isifo uEnoki esithi: Pathogenesis

Oku kusekelwe nangokurhala ezikumila kunje iinqanawa ezincinane igazi emithanjeni. Ngenxa yoko, oko exuded plasma kunye neeseli ezibomvu ibekwe esikule ezingqongileyo. picture izilonda Histopathological phantse ziyafana periarteritis nodosa. Kodwa ezo iimpahla eyonakalisiweyo ukopha vasculitis, kakhulu.

isifo uEnoki esithi: iimpawu

Ichaphazela abantu ikakhulu abatsha. Ukukhokela uphawu - kwamaqhakuvana apha emilenzeni kunye nomlinganiswa exudative-ukopha. La maqhuqhuva abe zobungakanani ezahlukeneyo, kodwa ngokubanzi amancinci symmetrically luhle. Ngumlomo Idla ziintlungu joint, ukurhawuzelela, oluthile, kwaye ukunyuka kwamaqondo obushushu xa iyonke. Ukuba isifo kunzima kakhulu, ngoko ke bandlala kwaye bahlanganisane ukuze iindawo ukopha enkulu. Kungahle opha ukufa kwimimandla emikhulu. iintsuku 10-15 emva ukujaduka ngokuqhelekileyo luqhubeka, kodwa ngonaphakade. ukuba kuyabuya njalo. Ngenxa nokudumba periarticular, utshintsho kwamalunga. Ngamanye amaxesha isifo uEnoki kukaThixo nzima nangakumbi legazi ancedisana kunye nezibilini. Ukuba oko kwenzeka ngexesha esiswini namathumbu, nesisu ukuba iintlungu ezibukhali. Brain ukopha ihamba kuphuhliso ukukhubazeka kunye paresis. Ngamanye amaxesha iinguqu okufana ukopha vasculitis, kwenzeka nje kuphela enyama yangaphakathi, kunye neempahla ngegazi retina kwaye zichaphazela amehlo kunye nenkqubo luvo.

isifo uEnoki esithi: imilo

Zezi ezine: samathambo, imibane-fast, kulula, kwaye esiswini purpura. Ngamnye kubo uneempawu zaso. Simple purpura, umz, ephelekwa njengamaqhakuva ukopha kwi nesikhumba ngenwebu yangaphakathi. Ivela ku oluthile jikelele, ubushushu. Kwiinguqu purpura samathambo kwenzeka amalungu (idla idolo). Baba buhlungu kakhulu, adumbe. Kakhulu eqhelekileyo kubantu abatsha kunye nabantwana kwenzeka purpura esiswini. Xa kuvela ukopha namathumbu emathunjini. kakhulu esiswini ngayo uhlaselo. Ngokulenza admixture waphawula igazi, ilindle ungalibali. Onke la zikhatshwa ukunyuka kwamaqondo obushushu emzimbeni. Ngelo xesha apho kunye ukujaduka isici. Ngaphantsi bavame ezandulela esiswini syndrome okanye zenzeke emva. purpura Fulminant na iimpawu ezifanayo, kodwa ngokubanzi kunzima kangaka ukuba ukususela kwimihla yokuqala kunokuphumela ekufeni.

isifo uEnoki esithi: ukuqaphela

Kubalulekile ukuba yokuzohlula evela kubazali kunye purpura thrombocytopenic. Ngokomthetho isekelwe phezu ubukho exudative ukopha kwamaqhakuvana ezithile ze-yaziwa kakuhle, iintlungu edibeneyo izifo ngokubanzi. Ukuqwalasela iziphumo analyses kufuneka athathe ingqalelo inani zegazi - baba eziqhelekileyo, akukho tshintsho kufuneka babe izalathi si zokunikwa coagulation igazi, ucinezelo ye ihlwili legazi.

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