Isifo Hirschsprung esithi: iimpawu ebantwaneni, photo, oonobangela, isifo, unyango

Enye ezimbi abangabelwanga yi sisifo Hirschsprung kaThixo. Iimpawu kubantwana zibonakaliswa kwesisu rhoqo. Ngamanye amaxesha sifo zenzeke abadala. Kodwa uninzi bonke abantwana abaphethwe kulo. Sisifo naso into njengelifa. Oku kubonakala kakhulu amakhwenkwe. Ebonakalisa ngoko nangoko emva kokuzalwa. Xa unyango kuphela ungenelelo olusebenzayo yotyando.

zokugula Uphawu

Isifo uchazwa 1887 yi wabantwana Danish Harold Hirschsprung, ogama kamva esi sifo yaye igama. Ekuqaleni, le meko ebizwa ngokuthi gigantism wamathumbu. Pathology elinye igama. Ibizwa iziphene agangliozom wamathumbu. Yintoni isifo Hirschsprung xa abantwana?

Iimpawu (photo ubonisa ngezifo) ziya masikhokelwe kwiimpawu ngamnye, abandinyelise ngawo iindonga colon abafumaneki ngamabona ganglia luvo. Ezizezi ziyayilawula izihlunu bayacalulwa ukwenza ukutya yi emathunjini. Ukungabikho ganglion-luvo ebangela ijwabu kwezihlunu ukuba engasebenziyo. Ngenxa yoko, ukutya na ukuhamba ngapha Amathumbu amakhulu. Le ngezifo kuthiwa sisifo Hirschsprung kaThixo. Iimpawu kubantwana ichazwa njenge ukuqhina, usuleleko kunye nokudumba.

Iziganeko sifo Hirschsprung kaThixo - 1 ngo 5000. Loo yenye kuzalwa amawaka amahlanu kuphela ubunzima kwesi sifo. Isikakhulu sifo, njengoko kubonisiwe ngentla, banesifo emakhwenkweni.

Kubanga zokugula

Nangona sifo kuchazwa 1887, kwaqengqeleka iminyaka emininzi ukuchonga unobangela ukuvela nophuhliso kwesi sifo.

Oogqirha ukunika imithombo emininzi ukuba bawaphikise uphuhliso izifo ezingemnandi ezifana nesifo Hirschsprung kaThixo ebantwaneni.

Ubangelwa sifo:

1. Ngenxa yophando yaye yasekwa ukuba ukuyilwa leengxaki kwenzeka nokuba Esibelekweni. ezisebenzisanayo Nerve, nto leyo iza kwenza imisebenzi eyimfuneko ukudla, akhiwa kwimveku ukususela kwiiveki ezi-5 ukuya ku-12 zokukhulelwa. Kwiimeko ezinqabe kakhulu, uphuhliso iiseli zemithambo kwinkqubo yokwetyisa komntwana ayiphelelanga. Kulo Amathumbu amakhulu, ukuba ayakhekanga. Izinto ezibangela le sifo nangoku kucaciswa. Kukholelwa ukuba oko wabonakaliswa zofuzo DNA.
2. Phawula kwakhona ufuzo kwi livela kwesi sifo. Ukuba kukho iimeko esi sifo entsatsheni, ngoko ke amathuba okuba umntwana oya kuzalwa efayo, akunto kakhulu phezulu. Ingakumbi ukuba umbungu eyindoda, kuba makhwenkwe nokubandezeleka kulo sifo izihlandlo 4-5 kaninzi ngaphezu amantombazana.
3. Kwiindawo apho kukho lwakukhula radiation, abantwana abaninzi bazalwa kunye nesifo Hirschsprung kaThixo.
4. Factor echaphazela yimbonakalo sifo Phantsi engqondweni.
5. Pathology bangaba ngenxa yokuba ukuphazamiseka yonyango kwi unina.

nokubekwa kwezifo

Kukho iintlobo ezininzi kule ngezifo njengoko sifo Hirschsprung kaThixo (kubantwana). Iimpawu ezibonakala ngayo umntwana, inokuba sikombisa uhlobo sifo.

Kukho ezi fom zilandelayo sifo Hirschsprung esithi:

1. Ingahlawulwa - nokuqunjelwa zenzeke esemncinane. Ukumelana nabo ngokusebenzisa nyulu enemas ixesha elide.
2. Subkompensirovanaya - enema akanalo isiphumo lula. Ngenxa yoko, ukuthotywa kwenzeka ukuncitshiswa weight. Isigulane uziva noncwino neentlungu esiswini. Kule fomu kwesi sifo elifana neli ukubonakala dyspnea, igazi. Lokugaya ivavanywa utshintsho olubalulekileyo.
3. Isifo sombefu - yethumbu ayikwazi mayicocwe enemas ukucocwa laxatives. Emva la manyathelo, imvakalelo ubunzima esiswini ezisezantsi ukuqunjelwa musa ukuma. Xa utshintsha ekutyeni okanye umthambo onzima esemzimbeni ukuphuhlisa ebukhali emathunjini. In-isigulane abantwana olu hlobo sifo lubekwe losuku kunye nya.
4. Acute - wamathumbu isithintelo kwiintsana.

zesifo sifo

Isifo kunokuzibonakalisa ngemihla yokuqala yobomi. Umzekelo, ukuba amathumbu hayi qho sosana ngemihla yokuqala yobomi, kuyimfuneko ukuhlola usana ukuchonga unobangela kwaye isifo. Mhlawumbi oku sifo Hirschsprung kaThixo.

Iimpawu ebantwaneni, ngubani kufuneka sinikele ingqalelo, khangela like this. Umntwana ala ukutya. Umele ukuba nokuqunjelwa. Amathumbu ngeke qongqololo. esiswini kalanga. Kukho kwesifuba. Oku kubonisa ukuba isifo umntwana Hirschsprung kaThixo. Iimpawu kubantwana kwenzeka, ngokuqhelekileyo phakathi kwinyanga yokuqala yobomi.

Nangona kunjalo, esi sifo ungenza ngokwayo waziva kamva. Ngoko ke, kufuneka ngokusondeleyo esweni imo iintsalela yempilo. Uqhagamshelane ngokukhawuleza oogqirha zakho xa ubona imiqondiso efana nesifo Hirschsprung kaThixo ebantwaneni.

Iimpawu wezifo ezinokwenzeka kwiintsana phantsi konyaka:

• nokuqunjelwa;
• ukulibaziseka ekuzuzeni ubunzima;
• i wakrwada kwe isisu;
• ukuphalaza;
• norhudo.

Ukuba nokwenzeka isahlakalo esi sifo babonakaliswa kamva ebomini.

Ehamba oluthile ezilandelayo iimpawu:

• nokuqunjelwa ezingapheliyo;
• isihlalo ngaphandle yimivumbo;
• yethumbu sakhulula soze ngokupheleleyo.

Yintoni enye ukuze sinikele ingqalelo?

Uphawu engundoqo isifo emathunjini emikhulu ukuqhina ezigulo ezondeleyo. Xa ukondla lwebele luphawu ukuze kungenzeki. Iimpawu abuhlungu kuvela kuphela ngexesha kukutya angqinelanayo eyaziswa ezityiwa kwiimvuthuluka. Kuwukhulula isicelo i enema. Kodwa kwamnceda liyasetyenziswa kuphela usaqala. Emva koko sebenzisa i enema uyayeka ukunika isiphumo oyifunayo.

Tshintsha ubukhulu kunye nokumila esiswini, ibekwe isisu ephantsi-Natal, Limpopo nakuwo - yinto kwakhona neziphawuli ulingana ukuhlawula ingqalelo. Xa uphuphume asuswa colon kunye nesisu ithatha imilo yezi ezitenxileyo ezinokwenzeka.

Ukugabha okwenzeka kwesi sifo, kunceda umzimba ukuphelisa isitulo, yingozi kuye.

isifo Hirschsprung kaThixo kungabonwa nayo nasebudaleni. Ezi zigulane zidla ubunzima ukusuka kwesisu ebuntwaneni. Kufuneka iyeza ukunceda intshukumo kwesisu. Bayakhalaza buhlungu gqolo apha esiswini, badla ngokujongana flatulence.

uxilongo zokugula

Kubalulekile ukuchonga ngokukhawuleza esi sifo.

Uxilongo izifo Hirschsprung xa abantwana iquka iindlela ezifana:

1. iimviwo efakwa. Kutyhilwa isikali igutyana engenanto. Kukho umsebenzi bhetele indlela sphincter.
2. Sigmoidoscopy. Efumanise imiqobo iindawo engqongqo isikali, okanye ukungabikho imali encinane ngendle.
3. X-ray. Ibhaqa nethumba nokunyusa yomtya ye ikholoni.
4. Ergography. amasango ikholoni Linyuke ku 10-15 cm ubukhulu. Zisebenza lonke kwisisu.
5. Indlela barium nokunqunyanyiswa. Iarhente nshita udlula iphecana zesisu, bazondelele kule ngekhefu. Ukusuka apho ke ixesha elide ivakale ilumeza. Ngamanye amaxesha ulibele ukuya kwiintsuku ezi-5.
6. Ultrasound indawo emathunjini.
7. Anorectal manometry. uxinzelelo kulinganiswa ethunjini.
8. Kolonosokopiya. Kuqinisekisiwe okanye ukulahlwa data eyayibonisa X-ray.
9. A biopsy kodonga efakwa for Swanson. Ikhethwa ubukho luvo ganglia kwi ikholoni ngokuthi utsala Isiqwenga colon eludongeni.
10. Histochemistry. Icwangcisa umsebenzi inwebu enzyme acetylcholinesterase.

unyango elondoloza

Musa ukuthembela therapy ezinjalo. unyango isifo Hirschsprung xa abantwana oluqhutywa kwiimeko ezininzi kuphela uqhaqho. unyango Conservative ngokubanzi ukhonza kulungiselelwa ahlinzwe.

unyango zokuzilola kubandakanya:

1. A isondlo, ukutya. Kucetyiswa ukuba sidle imifuno, iziqhamo, iimveliso zobisi, ukutya loo nto ayithethi ukuba ukusekwa igesi.
2. Massage, ukuyifundisa, imithambo. Yenza motility emathunjini.
3. Zokuhlanjululwa enema.
4. Ulawulo efakwa of imithi proteinaceous kunye nezisombululo electrolyte.
5. Mzimba.

unyango ngotyando

Oko kukuthi, ivumela isigulane emva kwisimo balahle sifo Hirschsprung kaThixo.

Ubudala kakhulu efanelekileyo komntwana kutyando kuqwalaselwa iminyaka 2-3. Lungisa sesigulane utyando ekhaya. Kwiiveki ezimbalwa, kufuneka ulandele ukutya, iintshukumo kwesisu encediswa enemas. izidlo Special ngokuyimfuneko isincomo yi igqirha khona ethathela ingqalelo ubudala umntwana zonke iimpawu zomzimba, kwakunye nqanaba uphuhliso esi sifo krakra njengokuba isifo Hirschsprung kaThixo ebantwaneni.

Emva kotyando, usana kufuneka kubonwe ngugqirha phakathi kwiminyaka emi-2. Ngeli xesha, ugqirha wenza ukutya ngamnye umntwana wakho. Abazali kufuneka sigcine iso esitulweni usana. Kucetyiswa ukuba kwiimvuthuluka enema yonke imihla, kwelinye kunye nexesha elifanayo. Kuyimfuneko ukuba ukuphuhlisa intshukumo kwamathumbu reflex.

isiphelo

isifo Hirschsprung nako kuyingozi. Kunokubonakaliswa kwangoko. Kulo mzekelo umntwana ukubandezeleka kwiintlungu esiswini, ubucaphucaphu, ukugabha, ixesha elide. Abazali kufuneka esweni rhoqo kwesitulo kunye umntwana nje iintshukumo zokwaphulwa kwemithetho encinane hamba uye kwagqirha.