Isifo bone Marble: oonobangela, iimpawu, unyango, uthintelo

Marble i ngezifo yesifo azalwa olubonakaliswa osteosclerosis ehlasela uninzi amathambo skeletal kunye notshintsho ezinzulu calcium-phosphorus ukutya. Esi sifo kunqabile kakhulu. Kuye kuchazwe okokuqala ngo-1904 yi ugqirha waseJamani kunye ray Albers-Schoenberg (Albers-Schonberg NE). isifo Marble kwenzeka ngokupheleleyo kuzo zonke iindidi ubudala, kumazwe kulo lonke ihlabathi, ngokufanayo nobudala.

Esi sifo eziliqela ntonye - osteosclerosis enaso, osteopetrosis, kunye dysplasia giperostaticheskaya isifo Albers-Schonberg. Musa ukubhidanisa sifo marble kunye syndrome ebizwa ngokuba "isikhumba ibhastile." Xa isifo bone emarmore asemzimbeni iqalisa ukuvelisa into compact extra, kwakunye kwi emjelweni medullary uqala ukuphuhlisa kwintsunguzi ithambo. A emarmore emhlophe, into ebizwa impahla yesikhumba vazonevroz naso eluswini, kaninzi kwenzeka ebantwaneni yaye kubonakala amabala reticular kwi nolusu umbala oluhlaza emva ucimayo. Emva ukufudumala uphawu inyamalala. Kwakhona eyenzeka eluswini abadala marble kunye isikhumba esibhityileyo ukukhanya abanengxaki imithambo yegazi.

Le umyalezo yale sifo ayaziwa. Kwiimeko ezininzi yaziwa sifo ngayo umlinganiswa usapho ezimbejembeje luyasuka kwizizukulwana ngezizukulwana. isifo lakhe igama marble unetyala umfanekiso ekhethekileyo-X reyi ngamathambo, nto leyo luchazwa ngumntu ukufana engaqhelekanga kunye kwamathambo ezibukhali, kwakunye nokungabikho amathambo. Kubonakala ukuba amathambo zenziwe lemabhile.

Kukho iintlobo ezimbini nezemarmore sifo:

- elibaleka akukho iimpawu ezibonakalayo lwezonyango, wafunyaniswa kuphela iimviwo X-ray;

- kubonakala kubantwana abancinci, zomlomo iimpawu.

Olona phawu iphambili sifo ukuqaqadeka okuqhubekayo okanye olungaphelelanga kwethambo trabecular. Xa lokuqala sifo sclerotized kuphela amathambo tubular kwi metaphyses amathambo kwaye iflethi kwi izabelo peripheral. Ngaphezu koko, uchonge itywina ithambo cranial olungalinganiyo, kwisisu paranasal ikakhulu abachaphazelekayo, ingakumbi eziziiprayimari ngokungqalileyo. Hlula kwakhona kungafihlwa yaye emihlathi, oko kukhatshwa ephula dubulo nezinyo nophuhliso - ukutshintsha ubume babo, iingcambu aphuhliswe ngokwaneleyo, lokutshabalalisa imijelo kunye nemingxuma ze yezinyo laso. Kaninzi izigulane funa uqwalaselo lwamayeza unobangela iintlungu imilenze nokudinwa xa behamba. bamathambo Marble nayo echaphazela uphuhliso olujikeleza, njengoko ukukhula ngokugqithisileyo esiqwini ithambo engaqhelekanga ngcembe indawo esikule hematopoietic.

Best sifo iziphumo ukuphatha emarmore zifunyenwe kuzinzame nokufakelwa (nokufakelwa) lomongo wethambo. unyango Ngokwenene ngempumelelo esi sifo ayifuni ezikhona. Unyango lwesi sifo kakhulu ezijolise ekolulweni iinkqubo kwimisipha luvo, babathwalela kwiimeko ezininzi njengoko OPD. Izigulane kubonisa ukuyifundisa massage kunye nokuqubha. Nutrition kufuneka ibe ngokupheleleyo, ninendyebo izinto umkhondo kunye neevithamini, kufuneka babekho kule menu, itshizi, iziqhamo kunye nemifuno, iziqhamo zendalo kunye ayo yemifuno. Abantwana nalo kwesifo ithunyelwe athile kunyango kweso sibhedlele.

Iindlela ezisisiseko lokuthintela marble sifo enxulumene ebambe kokumitha osana diagnostic iiveki 8. Ukuthintela kukuvela sengozini bone kunye Ukophuka zophendlo lwezifo kufuneka yenziwe iimviwo onamandla zamathambo.