Iimpawu ezinxulumene hemolytic-uremic syndrome kunye nonyango yayo

Ngoko ke, into ekufuneka uyazi kuqala ngenxa hemolytic-uremic syndrome (olufinyeziweyo - Hus). Oogqirha bathi oku sifo kakhulu iimpawu ezintathu: ukusilela etsolo kwezintso, igazi hemolytic, thrombocytopenia. Kufuneka kuqatshelwe ukuba umgaqo yokugqibela ngokuqhelekileyo ibonakala ngokucacileyo. Isifo unesifo ikakhulu kubantwana abaselula.

izinto kunokwenzeka

Eyona ezisemqoka athe anxulunyaniswa hemolytic-uremic syndrome - ukusabela Andidibani amayeza, kwakunye igciwane lohlobo. Ngoko kusengqiqweni ukuba esi sifo uqala ukuphuhlisa emva izifo zemiphunga kunye nesisu oyingozi okanye izigulane abafumana antibiotics. Ngokumalunga Pathogenesis of Hus, kule nkalo, kubaluleke kakhulu iqhotyoshelwe ubukho basabele sokuhlasela. Kwezinye iimeko, ukuze nokuba kuphakame microangiopathy systemic.

symptomatology

Ziziphi iimpawu zidla zibangelwa hemolytic uremic syndrome? Kufuneka kuqatshelwe ukuba ekuhambeni sifo ngoogqirha ngokuqhelekileyo izigaba ezithathu. Okokuqala, prodromal, buya kuhlala ukusuka imini enye ukuya kwiiveki ezimbini. Okwesibini, babizwa ngokuba "ixesha lobunzima" - ukusuka kwiiveki enye ukuya kwezintathu. Emva koko kufike ixesha ukumimitheka (okanye ukufa) malunga nesigulane eso.

Inxalenye yokuqala sifo xa iyonke kufana ityiwe lukhatshwa iimpawu ezifana ukugabha, iintlungu kakhulu isisu, urhudo kunye nentwana yegazi. Ezinye izigulane kweli nqanaba ophawulwe unditsho, ukozela kunye nokulahlekelwa sezingqondweni. Emva kwethuba prodromal xa izigulane ezininzi kuza bachache ebonakalayo. Neengcali haemolytic uraemic syndrome ezinxulumene njengoko igazi haemolytic, thrombocytopenia, kunye izilonda sezintso. Oogqirha bathi ukuba umfanekiso lwezonyango, njengoko umthetho, zizakubalulwa a polymorphism. Kwezinye izigulane, iimpawu ukuze kulawula ntlekele hemolytic, abanye - iimpawu ahlekise ukusilela kwezintso. Common kuzo zonke iimeko ingqalelo luphawu igazi hemolytic - elivela ngayo phakathi Hus.

Hemolytic-uremic syndrome ebantwaneni sesibini isigaba lubonakala ngokuba pallor lokufa ulusu. Phambi senyongo kungabonwa hyperbilirubinemia. uvavanyo Direct Coombs 'idla negative, ihemoglobin bewuhlisele, inani erythrocytes lincitshiswe. Kwakhona, izigulane ngokufuthi impumlo owophayo.

ekuxilongweni

Oogqirha ngokuqhelekileyo ukuxilonga Hus, ngokusekelwe kwindlela ezintathu eziphambili: ubukho igazi hemolytic, thrombocytopenia purpura kunye uremia. Ngokubanzi, umfanekiso yinto embhoxo Moshkovitsa syndrome (isifo sezintso, igazi egazi iimpahla, njalo-njalo. D.), Ngenxa umahluko kuphela isesokuba yokugqibela ngokuqhelekileyo kubonakala kubantwana abadala, kunye mikrotrombozov kwenzeka ubukhulu becala entliziyweni wesibindi.

Hemolytic uremic syndrome: unyango

Ingcinezelo autoaggression - yiloo njongo iphambili yonyango. Njengomgaqo, oogqirha wathumela yonke imikhosi, ukwenzela ukuthintela coagulation intravascular. Kulungile ukunceda lweeHedfowuni kunye prednisolone. Ukuba iyeza swi nga pfuna, oko kuboniswa olugqitha esikhumbeni.