Ichthyosis yesikhumba: oonobangela, iimpawu, unyango

Medicine abelwe iqela elahlukileyo zezifo, nto leyo ibangwa utshintsho kule nwebu amane ulusu kwinqanaba yemfuza. Ngenxa ukunyhashwa ulusu ivavanywa utshintsho oluthile kwaye lube efana ezikalini iintlanzi. Esi sifo ilifa kwaye kunokuzibonakalisa nangaliphi na umntu ubudala, kungakhathaliseki ukuba ngabaluphi uhlanga, isini kunye nobume ekuhlaleni. Ichthyosis lungabonakaliswa kakubi kwaye ayihlangulwa kwisigulana naziphi na iingxaki kwaye babe kunye kukhokelela ekufeni. Izifo ichthyosis nesikhumba ichthyosiform babe iintlobo ubunzima kunye, ngelishwa, zixhaphakile kakhulu kwaye kube nzima ukunyanga. Abaninzi eziphambili iilebhu zonyango basebenza nzima ukuze kunqandwe thile ngezifo kwaye ukwenza ubomi lula kwizigulane.

Yintoni ichthyosis

kumiswa engaqhelekanga le corneum ezinawo - ichthyosis. izinto zayo ngenxa ezingaqhelekanga kwi ikhowudi yezofuzo ye omnye okanye bobabini abazali - oko kukuthi, kwi-X-chromosome. Kukho izifo ezininzi azibonakali kwaye khangela ngathi ichthyosis, kodwa enyanisweni akunjalo. Ngokuba ukwesaba ekuchongeni kwi iimpawu ezifanayo ayikho imfuneko. Isifo real kunokusibonisa oyingcaphephe kuphela, kwaye uninzi lwazo ezifana izifo ulusu awusenayo ngempumelelo. ichthyosis kunye nesifo solusu ichthyosiform sezineentlobo ngeentlobo, kodwa iyeza ngokomthetho wahlula ngokwamaqela eziliqela. Funda ngakumbi malunga ngamnye kubo - ngezantsi.

ichthyosis eqhelekileyo

Kwakhona ngokuba ichthyosis vulgaris, yenye yezona eziqhelekileyo iindidi. Isifo kubonakala besebancinane, kodwa, ngokungafaniyo nezinye iintlobo, ngaba ungambethi abantwana phantsi iinyanga ezi-3 ubudala.

Esi sifo ndlongondlongo uziphethe ngexesha nokuvuthwa ngesondo yomguli, kwaye malunga ne-10 leminyaka ubudala. Xa hormone kuzinziswe umntu, kuza nokuphucula imeko yesikhumba. Abanye isiqabu kufika ngexesha ehlotyeni, kodwa esi sifo snap ebandayo iqala inkqubela. Amakhwenkwe kunye namantombazana kunye amathuba alinganayo ukuze oku sifo. ichthyosis eqhelekileyo ophezulu ukusuka yenethiwekhi (omnye umzali) umntwana. Isifo luwusukele nomonde ubomi, imeko ukuze kuphuculwe yaye zimbi kakhulu.

Iimpawu ze ichthyosis vulgaris

Ichthyosis vulgaris Igama layo yalifumana ngenxa yokuba yayibonakala ukuqhayisa. Esi sifo sichaphazela eluswini, izidlele, ibunzi nemilebe imisele ngakumbi. Isikhumba igutyungelwe ezikalini ezincinane ezimhlophe sisinyanzelo iliso. ukubonakala kwazo kwaye ezimile ingqolowa, ngokuba ichthyosis lolu ulusu kuthiwa "pityriasis enesitshanguba". kwiindawo ezichaphazelekayo abekho phantsi kwaqapheleka okanye ukudumba, kodwa isikhumba ndomisa icolekile. Isifo alichaphazeli iinwele okanye izikhonkwane omdala nomonde yaye abazange kubangela ingxaki enkulu.

Face - kuphela indawo yokuqala indawo, ngokuhamba kwexesha, exobukayo kuthatha ngokupheleleyo indawo, kodwa ngayo kwezinye iindawo zomzimba. Idla ngokuba kwedolo engqinibeni, esinqeni kunye indawo umva ongezantsi, maxa wambi neqatha. Oku asizichaphazeli ichthyosis, ngokungafaniyo nezinye iintlobo, indawo nasemiphakathweni kwaye ubeka nezibaya isikhumba enkulu. Ngu uhlobo sifo yaye ubukhulu kunye nokumila kukubola eqhelekileyo ichthyosis ulusu zahlulwe iintlobo: ichthyosis elula, xeroderma yeNyoka, inaliti, emnyama kunye akhazimlayo (pearlescent) ichthyosis.

imiba enxulumene

abantwana abancinci kunye nabafikisayo ubunzima ichthyosis embi kakhulu. Ezi zizathu njengoko ukunyhashwa amalungu kunye neenkqubo zomzimba.

• Umntwana kancinci ukukhula okanye ukuzuza ubunzima, ikhangeleka emboxo, ezinxaxhileyo kuphuhliso engqondweni.
• secretion lokuwandisa sebum kunye nokubila, ngenxa yoko - isakhiwo unwele yaphulwe, ukuba uwe. plates Nail yaba buthuntu, ezingcakacileyo, krobo.
• Buthathaka inkqubo yomzimba yokuzikhusela, yaye ngenxa yokuba abantwana abaphethwe zizifo ezosulelayo arhabaxa.
• ukutya nothuke ihomoni ukutya.
• Le yegazi liyaphuma, nto leyo ke ekhokelela izifo kwenkqubo sentliziyo olujikeleza.
• Ukuphuhlisa "ukungaboni" - isimo apho abantu musa ukwahlula izinto ebumnyameni.

Zonke ezi ngxaki kwacaca ingakumbi ngexesha lasebusika. Kuyimfuneko ukuba anikele ingqalelo ekhethekileyo kwisondlo nempilo. Ingaba umoya luncedo IiReggaeton ilanga.

ichthyosis eziqhelekileyo ifomu sofuzo

Esi sifo ichthyosis sofuzo ngendlela eboniswe ekubonakalisweni eyomeleleyo yonke yesikhumba iyaxobuka emzimbeni yonke kwaye abopha ngokwesini: ubunzima le fomu abameli eyindoda kuphela. Amantombazana zinikwe abagulayo, kodwa abathwali. Oomama, ukuba adlulisele esi sifo koonyana bakhe, emva koko sikhupha chromosome ilifa neentombi zabo. Ngoko qhubeka ngonaphakade.

Kuba amantombazana uhlobo sofuzo esi sifo kunokuba yingozi. Kwiimeko ezinjalo zinqabile yaye kwenzeka kuphela xa abazali bakhe bobabini baye abosulelekileyo, ngoko ke uya pathologic intombi X chromosome. Esi sifo kakhulu kunene, la mantombazana kunqabile asinde.

Iimpawu ifomu sofuzo

Rhoqo sifo Nentloko enesihlwitha yohambayo, ukuxozwa iinwele, unako ukuza nenkqayi ngokupheleleyo iphuma. Ishq ezinkulu shinyi, ngokungafaniyo iifomu inhlamba kukho umthunzi mnyama. Izigulane abaneengxaki amalungu. Ngamana ukuphuhlisa iingxaki bone kunye ukukhubazeka engqondweni, corneas lisibekele, kukho amatyala ukuxhuzula.

ichthyosis naso obunzima

ichthyosis azalwa - le ngezifo olunzima kakhulu, zisenokungabi qatha okanye kakhulu. Ipesenti ukusinda oluncinane kakhulu, abantwana zibulawa ngaphakathi kweeyure ezimbalwa emva kokuzalwa. Kwiimeko ezinqabe kakhulu, umntwana uyakwazi ukugcina. Isifo izitshintsha zibe ngeendlela ezahlukeneyo, erythroderma, umzekelo. Kwiimeko ezinqabe kakhulu, nto leyo linokubizwa ngokuba ngummangaliso, esi sifo ukufiphala ngokupheleleyo kunye nobudala kunye nomntu nakakhulu nexhala.

Iimpawu kakhulu

ichthyosis azalwa kubantwana esizibonakalisa eziliqela iingxaki kunye malformations. Aba bantwana bazalwa ngaphambi kwexesha, kunye enobunzima obuncinane. Ulusu baby emuva kufana nezikrweqe, enika neentanda yaye oluphuma igazi.

Ngelo xesha xa uphuhliso nolusu yomntwana yaphulwe, amalungu enye, ancedisana yencindi kuqhubeka ukuphuhlisa ngokuqhelekileyo. Besikhumba ilastiki, siqulethe etyekayo eqhotyoshelwe eli laphu ngaphandle. Ebusweni bonke umzimba lo mntwana gqitha kakhulu kwaye bathathe imbonakalo nemvelo.

Isizathu sokuba izinga lokusweleka omkhulu kuzalwa ngenxa yokuba izinto zenziwe ngekeratini uyakhula notsalo okanye ngokupheleleyo izihlangu amalungu abalulekileyo. Olusanda kuphefumla udle, amalungu zangaphakathi kufuneka iziphene kuphuhliso, usulelo enxulumene. Aba bantwana zibizwa ngokuba "harlequin", nezifo - ". Harlequin uphawu"

ichthyosis naso mnene

Ukuba ichthyosis azalwa iphuhlise enomoya form (nabungozi), itakane ufumana ithuba lokuphila. inyama Keratinized sikhula ongazanga uhlobo kakhulu. amalungu yangaphakathi, nokuba bathe gqitha, bayakwazi ukwenza umsebenzi wayo ebalulekileyo.

Iimpawu mnene

Ichthyosis yabantwana kuchaphazela ulusu lonke, okanye kumacandelo athile kuphela. Kwiindawo ezinjalo, isikhumba uba ebomvu, edematous iviwe ngezantsi itywina, ingakumbi kwiindawo apho imibimbi esikhumbeni. iindawo yezifo phezu kobuso inokuba babenza bubi imbonakalo, Ukucofa ezineziciko okanye impumlo kunye ndawo ngomlomo. Kodwa ke amathuba zokuziphilisa aba bantwana.

Ichthyosis ngohlobo "okhanyayo"

ichthyosis isikhumba edidekile ngamanye amaxesha kunye zoster iinwele. Ebonakalisa nemimandla apho isikhumba uyaguqa (amadolo, amalungu ingqiniba). Nakujoliso olutsha wayifulela maqhuqhuva ezincinane zinezihloko ezikalini ezinkulu shiny purple.

ukuvimbela

Ichthyosis - isifo solusu ukuba makangathintelwa, kodwa kusenokwenzeka ukuba ukuqikelela ngokuzalwa kwabantwana kunye sifo. Kwakukho a lot of amaziko zocwangciso ntsapho ezibonelela zemfuza ingcebiso. Iingcali iya kuthathela ingqalelo zonke iparameters, ingakumbi xa isibini oselula okanye izalamane zabo ziye amatyala ichthyosis. Genetics elinokuthelekiswa iindlela kunye nobungozi sifo kakhulu kwi kwimveku ze anike iingcebiso malunga nekamva yocwangciso umntwana. Ukuba iingozi phezulu, iplagi uncedo bangacetyiswa ukuba kuzalwa wosana olo. Kodwa ukuba kunjalo, esi sigqibo siza kuxhomekeka kuphela amaqabane.

isifo Ichthyosis ngohlobo kakhulu - sisifo esibi kakhulu. Inani leentsana ezifayo phantse 100%. Nokuba umntwana wakho uze ube nako ukusinda, akubonakali umgangatho zakhe zokuphila ingabizwa bekhululekile. Loo mntwana uya kuba nako ukuphuhlisa ngokuqhelekileyo. Yena uya kuba phantsi comorbidities ezininzi, yonke into iya ababangela ukubandezeleka ziintlungu. izibini ezitshatileyo kufuneka ubonise uxanduva kwaye hayi ukuba bangawutyesheli amacebiso kwiingcali.

unyango

Wena uxilongwe "ichthyosis"? Indlela yokuphatha kwesi sifo? Wazibandakanya unyango kunye nolawulo kwekhosi esi sifo, dermatologists, zemfuza, oogqirha kunye nezifo ezosulelayo. Okubuhlungu kukuba, esi sifo ibhekisela izifo yemfuza, kwaye akunakwenzeka ukuba ngokupheleleyo, lahlani kuyo. Amayeza uyakwazi ukugcina kuphela umgangatho wobomi isigulana kwinqanaba elifanelekileyo kwaye ngandlela zonke kunokuthintela ukuvela zosulelo. Abe kunye namafutha eziya ithambise iintsholongwane kommandla ochaphazelekayo, izigulana kuya kunyanzeleka ukuba asebenzise kubo bonke ubomi babo.

isifo ichthyosis untsonkothile nangokwengqondo. Kusenokufuneka kwengqondo, kunye nenkxaso ebalulekileyo labahlobo abasondeleleneyo. Kokukhatywa oluntu nga zisidimaze urhulumente sele kunzima yomntu. Abantwana kufuneka ukunxibelelana kunye noontanga babo. Kubalulekile ukucacisa ukuba abantwana ukuba esi sifo ayikho ezosulelayo kwaye ziyingozi kuzo.

Kuyimfuneko ukuba ukugcina nezifo. Power kufuneka ngokupheleleyo. Akukho nje, kodwa qiniseka ukuba uphephe tikaka kunye nobushushu. Ukubonisa ukuhlamba emanzini olwandle okanye ibhafu kunye netyuwa elwandle. Kuyimfuneko ukuba uhlale ukwentle impilo kunye nokugula encinane ukuya kufuna uncedo koogqirha. Usuleleko nakancane ungena umzimba elibuthathaka, ekwaziyo ngokukhawuleza zisiba sisifo esitalini iingxaki.

kwiindlela zakudala ukunyanga ichthyosis

Yamaxhwele aluleka ubunzima ngabo abaphethwe kwesikhumba enamaxolo. Yonke ezahlukeneyo kwaye zenzelwe ukuba ukunciphisa thile sifo nokunciphisa nobunzima. Nangona kunjalo, khumbula ukuba ukulandela icebiso labantu zithe zanokungqamana ethandabuzekayo ukuba amayeza, kufuneka zisetyenziswe ngononophelo. Ukuba ugogo kwimarike iya kuba kum ukuba iphambana na ichiza "evela izilonda ichthyosis Shleymana", nto leyo kwindalo ayikho, kungcono ukuba kulo "umqeqeshwa" kude. Kodwa amayeza apho emi ngokwenene izindululo. Ngokubanzi, aba iti neebhate phezu decoction wemifuno. Kukho zokupheka namafutha aqholiweyo ekhaya egxininisa ukuxovwa, isondlo nesikhumba kweentsholongwane. Bonke bephela zenziwe izithako zemvelo, uze upheke ekhaya kulula. Mhlawumbi uya ukhethe ngokwabo ezimbalwa iiresiphi esebenzayo ilula.

Ngaphezu efuna unyango abantu abaphethwe zizifo yemfuza, iimfuzo laboratory umsebenzi kumazwe amaninzi. Makhe ithemba ukuba unyango luza kufumaneka kungekudala, yaye siza kukwazi lokuphelisa uluntu sisifo esibi kwaye kuyingozi hlobo.