ZempiloDiseases and nemibandela

Syndrome CLC: iimpawu, iimpawu, unyango

syndrome CLC, eyaziwa ngokuba Lown-Ganong-Levine syndrome, kwenzeka nama-0.5% yabantu kwaye unobangela tachycardia ngo-30% amatyala, oko ke kunyanzelekile ukuba bafunde ukufumanisa indlela ubukho syndrome nendlela ukujongana nayo.

incazelo

Syndrome Unobhala-Levy Cristescu icala eyodwa syndrome of excitation ngaphambi ventricles zentliziyo, nto leyo luphawulwa yokuphumeza excitation ukuya ventricles kwiindlela ezongezelelweyo. yahlulahlulwe Intliziyo yomntu ukuze ventricles ngaphakathi imithambo, oko kuyimfuneko ukuze eyaneleyo kuzale igazi. Ukusetyenziswa kwale ndlela inikwa yi esiludumbo atrioventricular, nto leyo ifumaneka phakathi ventricles kunye nomthambo, kuso kukho ukubetha kwentliziyo esisezantsi kakhulu inikeza ukubambezeleka ventricular ukusikwa. Noko ke, abanye abantu ngendlela azalwa okungaqhelekanga yokwenza umlawuli angxamele ukuba yokucima esiludumbo atrioventricular, iindlela ezinjalo iinyanda kaYakobi, kwaye ifayibha uthatha Kent Maheyma. Ngezi Iindlela ngelixa ukubetha lifinyele kwaye kukho mkhuba CLC. Le ndlela ingabonwa enza uhlalutyo ECG. Le meko awukuchaphazeli ukusebenza entliziyweni yaye kuboniswa kuphela kwi cardiogram. Kodwa maxa wambi kukho iimeko xa kukho isetyhula ikhosi excitation. Oku kwenzeka xa, wacanda ngendlela anomalous, ubume ubuyisela nge esiludumbo atrioventricular, okanye ngolunye uhlobo - emva kokuphumelela umendo zaseprayimari, ibuyisela anomalous. Konke oku kubangela utshintsho kwisingqi nokubetha kwentliziyo, ke le nkqubo ibizwa ngokuba syndrome CLC.

Simanga kunye syndrome CLC ezi enaso, ukuze uqiniseke ukuba ezi ukungaqheleki ayaziwa. Kukho amacebiso ukuba kunxulumene ukuya kwizigulo zophuhliso Umbungu kwinqanaba kwentliziyo. Kwakhona, musa kulawula ukuba isizathu abe, kunye nezigulo yemfuza.

analysis of ECG

Uhlalutyo ECG kunceda ukuchonga le syndrome. Lubonakala yi ukuncipha PR (PQ) lekhefu. Le lokuphumla ibonisa ixesha apho excitation ufikelela myocardium ventricular ye imithambo kunye compound atrioventricular. Xa abantu kweminyaka engama-17 le lokuphumla okuqhelekileyo imizuzwana 0.2, kodwa kunciphiso lokuphumla, esinokubangela tachyarrhythmias, inokuba kwakhona imfuno lokufunyaniswa CLC syndrome. Ekubeni lo msebenzi syndrome Klerk-Levy Cristescu ngumkhuba eponymous luphawulwa kukuhamba anomalous channel ngokwentshukumisa - Yakobi umqadi osuka intendelezo kwinxalenye atrioventricular distal ye umchiza leyo ebangela kunciphiso PR lokuphumla (PQ).

Ukongeza ekwehliseni lekhefu wathi, ubukho CLC syndrome ECG akukho ezinye utshintsho. Ventricular entsonkothileyo (QRS complex - ecaleni kakhulu kwi cardiogram ebonisa elingaphesheya excitation ngaphakathi ventricles) aliveli gesiqhelo. CLC syndrome kaninzi kwenzeka abantu abantliziyo akukho ezinxaxhileyo.

iimpawu

Lo mkhuba uNobhala-Levy Cristescu akanayo mpawu, abantu abaninzi ngendlela uYakobi wayengazi nokuba sazi ngawo aphile ngaphandle nobunzima.

Iimpawu ze CLC njenge syndrome kuquka ekutshintsheni izinga intliziyo. Izigulana kufuneka badla ngesiquphe izinga lentliziyo ngokukhawuleza, nto leyo enokuthi ikhatshwe ukuqunjelwa, ndongenisa inyungu, isiyezi, ingxolo entlokweni yam. Ngamanye amaxesha kubonakala ndiyabila yaye Nanjengomvumbi phambi okanye emva kuhlaselwa. Kusenokubakho uVuyo spasmodic yanda.

unyango

Kwiimeko ezininzi, ezi syndrome CLC ayifuni ungenelelo olulodwa. Ngexesha ezikwenza isigulane intliziyo kuphela ukubanqanda kunye umyalezo okhethekileyo, zobuso okanye okupholisa natuzhivayas amanzi kwi dude, oko kukuthi, ukwenza Valsalva kushenxa. Ukuba ezi ndlela musa ukunceda, kufuneka ubize inqwelo yezigulana.

Kwakhona, xa kusingethwe maxa syndrome tachycardia zibangelwa yi-CLC, unako ukuqesha iinkonzo cardiologist, kufuneka lityumbe amayeza ezikhethekileyo, ezifana "Verapamil" okanye "Amiodarone".

Kwimeko apho ukuxhuzula tachycardia kuchaphazela ngamandla ubomi umguli, umsebenzi lwenziwa ukutshabalalisa uYakobi imiqadi ethintela setyhula drive stroke. imisebenzi enjalo ingozi, kwaye emva kokuba isigulane uyaqhubeka ngokukhawuleza kwi izilungiso.

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