Zempilo, Impilo yabantu
Okhawulezileyo ngabantu: Iimpawu and Treatment
ukusebenza ngokupheleleyo omzimba umntu akakwazi bacinge ngaphandle ukusebenza kakuhle kwe-kwamadlala ngesondo, ukuveliswa hormone. Naluphi na ukusilela kule nkqubo kubandakanya ukuvela izifo somatic. Dyslipidemia, yamafutha, ukutyeba, ischemia ingqondo - oku hayi kuluhlu lonke kubunzima kunokwenzeka. Zonyango iincwadi reference wafumana iinkcazelo ezininzi yokuhlukunyezwa enjalo. Umzekelo, intswelo wamatyhalarha androgen okanye insufficiency. Noko ke, phakathi kwabo, unyanisekileyo kakhulu kwaye kakhulu echanekileyo ingqalelo elithi "okhawulezileyo" ezingabantu. Ukuba le meko kuthetha, ngenxa yaso nasiphi na isizathu wokuba ngaba oko kuphiliswa - le mibuzo thaca iimpendulo eneenkcukacha kwinqaku yanamhlanje.
Inkcazelo emfutshane ye sigulo
Okhawulezileyo - isifo iphawulwa amadlala deficiency sex esebenza. Abameli besini sinamandla thaca ityhalarha asekhohlo nasekunene. Nature uye walungiselela ngokukhethekileyo bafundelane ngezibini ukuba inani labo. Wamatyhalarha ijwabu uvakalelo kwiingozi eyahlukileyo yokusingqongileyo. Kwimeko zokulahleka ubuchule ezisebenzayo komzimba kufuneka abe uhlobo reserve. amandla okungenisa amatyhalarha yinto eqhelekileyo.
Zazo eziphambili injongo - to yokuzala. Ukunqongophala ukukwazi ukuvelisa amadlozi emohluthayo umzimba lomntu oyindoda okuzala. IiNdlela ezinjalo ukwaphulwa ebekwe kwi lokuqala ukukhwelwa. Ngoko ke, nenzalo, ukuphuhlisa ngalo imvelaphi, loo nto ithathwa yingozi kakhulu. Buyisela umsebenzi iiseli ezingaqhelekanga kwithishyu wamatyhalarha nzima.
Okhawulezileyo in amadoda luphawulwa ezi mpawu zilandelayo:
- ukunciphisa kwinqanaba hormone sex;
- ukuncitshiswa lweempawu ubunjani kunye ubungakanani yobudoda;
- hypoplasia ye zangasese;
- nokuphazamiseka hormone wonke umzimba.
Ngokutsho manani, esi sifo of okhawulezileyo ngabantu kwenzeka ngo-1% yabantu ehlabathini. Nangona kunjalo, olu lwazi sethutyana, njengoko zithathelwa ingqalelo kuphela amatyala ezibhalisiweyo ngezifo. Unyango ngokuyimfuneko kwenziwe phantsi kweliso endocrinologist kunye andrologist. Uthomalaliso ihomoni ezininzi ezisetyenziswayo ngokuqhelekileyo. Xa yabelwa kwawo yotyando zeplastiki kunye zokwenziwa amalungu uhlelo zokuzala.
Eyona eziphambili ezibangela isifo
Ukuphuhliswa kwenkqubo zophendlo lwezifo lwenzeka ngenxa yokunciphisa inani hormone eziveliswa okanye ukugula biosynthesis. Zimeko etiological esi sifo zibandakanya:
- malformations bekhubazekile ebangelwa utshintsho kubume wamatyhalarha kunye / okanye tubules seminiferous;
- azinampembelelo ephilayo ityhefu oomama elizayo (utywala, inicotine, iziyobisi);
- baye radiation okanye ichemotherapy;
- ukusetyenziswa ixesha elide kwamadlala, iziyobisi antibacterial;
- izifo imvelaphi ezosulelayo (orchitis emva nemasisi, uqilikwane, vesicles);
- ngemithambo varicose le amasende;
- yokuhlala kwiindawo neemeko engentle yokusingqongileyo.
Izinto ezibangela okhawulezileyo emadodeni ukuba imilo kwenkqubo yezifo. Ngamnye kubo iphawulwa indima ethile.
imihlobo kwephulwa
Kuxhomekeka owona nobangela wezo isenzeko gonads ukusilela yahlulwe yobudala lokuqala, elesibini, wabiza njalo-. Zahlukene njani? Ifom ephambili esi sifo ebizwa ngezifo wamatyhalarha. Kulo mzekelo, njengokutyhoboza amatyhalarha ukusebenza ehamba phantsi kweempembelelo iimeko zangaphandle ezimbi. okhawulezileyo Secondary emadodeni inxulunyaniswa abanala makhwiniba kwisikimu "yebhinqa-yobuchopho". Le nkqubo iveliswa iihomoni unoxanduva nokusebenza amatyhalarha. Age okufana esi sifo uthathwa ukuba uhlobo ukuya exesheni eyindoda. izinto zayo, oogqirha abakwazi ukuchazela unanamhla.
Ulwahlulo ilandelayo isekelwe phezu xesha ebomini apho kwakukho yokugula. Le fom osandul luphawulwa inkangeleko yenkqubo zophendlo lwezifo kwisithuba zophuhliso zesibeleko. Prepubertal bene phambi ukufikisa (iminyaka 14). ngobuwena Postpubertatnom esi sifo kwenzeka emva kokugqitywa uphuhliso lweempawu zesini eziziisekondari.
Ezinikiweyo zesixa androgens eveliswe, ukwahlula iintlobo zilandelayo sifo:
- okhawulezileyo Hypergonadotrophic. Xa abantu, olu hlobo sifo esizibonakalisa ngohlobo wentshabalalo yethishyu wamatyhalarha wamatyhalarha. Oko kukhatshwa ukwanda kwemveliso hormone yebhinqa. Ngelo nezikhombisi ngexesha elifanayo testosterone yehla kakhulu.
- okhawulezileyo Hypogonadotropic. It luphawulwa kuyondelelaniswe Ukwehla gonadotrophins. Oku kunciphisa isixa testosterone zaveliswa.
- okhawulezileyo Normogonadotropic. Xa abantu, olu hlobo nkqubo zophendlo lwezifo kukhokelela uphazamiseko amasende, kodwa imveliso hormone yebhinqa eqhelekileyo. Isifo unxulunyaniswa ukutyeba.
Kuxhomekeka umyalezo anesiko ukwahlula iifom iziphene, sifumane idiopathic. Kwimeko yokugqibela, oyena nobangela wesifo kuhlala ayaziwa.
okhawulezileyo primary
Esi sifo kuba zombini ezifunyenwe kwaye bekhubazekile. Amaninzi, le leengxaki kwenzeka Esibelekweni. Boy ozalwa incanca encinane kunye kwisingxobo samatyhalarha ngokwaneleyo. Njengoko ukuqhubela phambili kumfanekiso kwezonyango eziguqulayo sifo. Xa amakhwenkwe elivisayo, ibonwa abatyebe kwafunyaniswa ukuba ibhaqwe gynecomastia lokuqala kunye nezinga eliphantsi noboya obuninzi emzimbeni.
Ezifuniweyo okhawulezileyo zaseprayimari amadoda senzeka komtshiso kwamadlala ZakwaLizwi phantsi ukuphazamiseka zilandelayo:
- orchitis;
- vesicles;
- epididymitis;
- mumps;
- unerhashalala.
Olu hlobo esi sifo ithathwa ukuba eqhelekileyo kakhulu. Senzeka omnye kwabahlanu amadoda ngaphambili isifo engazaliyo.
okhawulezileyo Secondary
okhawulezileyo Secondary inokuba iziphene okanye lufundiwe. Kwimeko yokuqala sifo landulelwa kuphuhliso secretion engafanelekanga yebhinqa kunye iihomoni hypothalamic. Idla kunye neengxaki genetic:
- Prader syndrome - Willie;
- syndrome Maddock;
- syndrome Pasqualini.
Ifom efumaneke isifo idla kubangelwa ukudumba meninges. Phakathi kwazo kukho meningitis, arachnoiditis kunye kobuchopho.
Iimpawu zesi sifo kubantwana abancinane
Lo mfanekiso kwezonyango inkqubo zophendlo lwezifo luqinisekiswa kakhulu ubudala yesigulane. uphuhliso yayo besebancinane ngokuqhelekileyo sikhatshwa mpawu zilandelayo:
- Disorder ezidalwa;
- evnuhoidizma ukuvela kweempawu (lokukhula eliphezulu ngokugqithiseleyo, amagxa ezincinane, imilenze elide);
- engekho imibimbi kwi samatyhalarha;
- ubungakanani elincinane lobudoda;
- gynecomastia.
Phambi enye okanye ezingaphezulu iimpawu adweliswe ngentla kufuneka kwaoko andibhekisanga ingcali yabucala.
Iimpawu zesi sifo abafikisayo
Uphuhliso esi sifo elivisayo luphawulwa iimpawu ezifanayo, ukuba prepubertal. picture lwezonyango angaba kunciphisa yobuntu kunye utyebile. Ukuze ubone ugqirha idla ibhaqwe hypoadrenalism kunye ndlala. Ngokwangaphandle, izigulane ulutsha wabonakalisa ngokucacileyo lokungaphuhliswa nkqubo dystrophy.
Iimpawu zesi sifo abadala
Okhawulezileyo in amadoda amadala ngaphezu kweminyaka engama-30 ngaphantsi kubi. Isifo ihamba yimbonakalo ezibayeni ezininzi wanamanqatha emzimbeni. Ulusu ngokuhamba kwexesha ngamandla okubuyela kwimo yaso yangaphambili wome. Kuyabonakala ukudinwa, lability ngokweemvakalelo, utyekelo uxinezeleko. Ngelishwa, le esibhedlele baphathwa ngamadoda kwiimeko ezingaqhelekanga. Ngokuqhelekileyo xa kufikwa ubudlolo okanye ukuphazamiseka umsebenzi erectile.
Le ukunqongophala ingqalelo impilo yabo kunokuphumela nemiphumela emibi. Inkqubo yezifo iqala ukusasaza nje kuphela kwinkqubo lokuzala, kodwa ngokuthe ngcembe ihamba kwamanye amalungu kunye namalaphu. Ukungabikho unonophelo abanobuchule kunokukhokelela nokukhubazeka.
iindlela isifo
Musa ukoyika ngenxa uxilongo ngaphambi kwexesha okhawulezileyo emadodeni. Ukuba le miba kuthetha ukuba uxelele ugqirha kwi yodliwanondlebe. Emva kokuba ukuvela kweempawu sifo kufuneka uqhagamshelane ngokukhawuleza uchwepheshe abaqeqeshiweyo. Nangona umfanekiso ngokungenamkhethe eliqaqambileyo lwezonyango, kuba isiqinisekiso esi sifo kufuneka bangenele uvavanyo clinical. Oku kuquka le misebenzi ilandelayo:
- zoviwo ngokomzimba;
- ultrasound zangasese;
- karyotype;
- urinalysis;
- isidoda;
- test igazi emzimbeni.
Le saveyi esabelwa isigulane ngamnye. Ngoko ke, uluhlu iziganeko zonyango zisenokuthi zahluke kancinane. ugqirha engqina okanye okhanyelayo uxilongo lokuqala ngokususela iziphumo ezifunyenweyo, unika unyango.
Iimpawu zonyango
Ukukhetha indlela ethile kunyango ukuya kugqirha kwaye uzimisele kuthathelwa ingqalelo oonobangela esi sifo. ukunyanga okhawulezileyo ngabantu lidla iinjongo ezininzi: ukulwa izifo, uthintelo ukungachumi, uthintelo isenzeko yamathumba kwi inyama wamatyhalarha.
Iifom bekhubazekile kunye prepubertal leengxaki soloko ilandelwa yi ukungachumi. Ukuyeka le ngxaki akwenzeki. Ukuba endocrinocytes egcinwe amatyhalarha, kucetyiswa unyango inkanuko. Abantwana ezimiselweyo iziyobisi hormone, kunye nabantu abadala - kumele androgens. Xa engekho hormone ezidalwe kufuneka ukuba basele ubomi.
Xa uhlobo secondary inkqubo zophendlo lwezifo gonadotropic emiselweyo iziyobisi izilinganiso encinane. Ukuba kuyimfuneko, baya kuhlanganiswa kunye testosterone. A indima unyango lwesifo bobabo imithambo nokufumana nezakhiwo vitamin.
Yonke imithi ezimiselwe ngamnye kuxhomekeka kubume bentlalo kunye nobudala isigulane. ukusetyenziswa unyango endaweni neearhente hormone ayikhuthazwa kwezinye iimeko. Ngokomzekelo, xa izilonda umhlaza endlaleni. Chronic isifo lung, ukutshaya, nokuphazamiseka amanqatha ukutya kunye umoya nokuhlaselwa - ezi Izimo isalamane. Kwezi meko, isigqibo malunga nokwamkelwa iziyobisi testosterone ethathwe ngamnye.
ukungenelela kuhlinzwa
Ukuba okhawulezileyo emadodeni ibangelwa abakhubazekileyo ngokwasemzimbeni kuphuhliso esini, ebonisa ukusebenza. Namhlanje, iintlobo ngeentlobo iinketho zokulamla esetyenziswayo ukuphelisa esi sifo. Umzekelo, kunye hypoplasia le lobudoda kusetyenziswa phalloplasty, kwimeko iba lityhalarha amdaka luyenziwa izembe. umzila we iba lityhalarha eyenziweyo kwenziwa ukuphelisa siphene mhle. Nayiphi na kwezi imisebenzi yenzelwa usebenzisa ubuchule microsurgical.
Sase- sokubuyisela
okhawulezileyo Primary, ingakumbi enaso, unako samiliselwa ngokungaphelelanga alungiswe. Oku malunga nokubuyisela le ubuchule yokwakheka kwaye kukwasetyenziswa yona lobudoda. Noko ke, yesilungu bunjani ukuchama ayikwazi ukukwenza. Ukhetho kuphela aphinde yokuzala - IVF amadlozi ngokusebenzisa ucingo. Ngaloo spermatogenesis vnutriyaichkovy kufuneka kugcinwe.
Enye sase- ulindele izigulane ukuba unesifo okhawulezileyo eziziisekondari. Ngabantu, ukunyanga esi sifo kwiimeko ezininzi ukunika iziphumo ezihle. Ngoko ke, oogqirha abakwazi ukubuyisela umsebenzi okuzala.
amanyathelo othintelo
Uthintelo engqalileyo yale sifo iye yaphuhliswa. Phakathi iingcebiso jikelele oogqirha bathi oku kulandelayo:
- unyango ngokukhawuleza nasiphi na isifo;
- ngokutya ukutya okusempilweni, ukungabikho imikhwa emibi, umthambo;
- odlulayo sihlolwe kwi 'yindoda' oogqirha njengenyathelo lokuthintela kanye ngonyaka.
Ezi ngcebiso, ngelishwa, akusoloko kusenzeka ukuba ukuthintela okhawulezileyo emadodeni. Xa lokuqala obubonakala kufuneka ngoko nangoko afune uncedo yincutshe. Ke ukusuka kwangethuba unyango kwenkcazo ugqirha, kamsinyane baya inkqubo impiliso.
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