ZempiloDiseases and nemibandela

Aplasia - a ngezifo enokuchaphazela naliphi na iqumrhu

Aplasia - ibonakalisa malformations foetal, nto leyo ichazwe kungekho nayiphi na inxalenye lomzimba okanye kumacandelo zeethishu. Le ngezifo kukuba zingahlukaniswa hypoplastic apho umzimba inokuba ebuntwaneni okanye lincitshiswe ngobukhulu kwaye simahla nesakhiwo obuqhelekileyo.

Yeyiphi le nto kukho ngezifo

Kufuneka kuqatshelwe ukuba aplasia - yesifo awazalwa enaso ukuba kwenzeka ngenxa yokuba ifuthe ekukhuleni kosana olungekazalwa ngqo okanye ngokungathanga ngqo nge emzimbeni kamama ngokomzimba, iikhemikhali kunye nezinto eziphilayo. Bona, esebenza kubazali gametes okanye izinyanya zabo, kunokubangela ukungaqheleki chromosomal kunye ukungabikho iqumrhu okanye kwithishyu.

Hi ndlela leyi, i engaphuhliswanga omnye sitho umbungu phantse ayinabantu kwaye ikhokelela enye umzimba ngokuqhelekileyo ukufa enxulumene. Ngokomzekelo, xa kungekho amathupha ureteric kwenzeka kakuhle kwezintso eziziisekondari aplasia, kunye m. P.

A umhla cut-off, emva koko iziphene ezichazwe kwi ndiseyimbumba asinakukwazi ukuphinda ukuphuhlisa, - le yinyanga yokuqala yobomi intrauterine.

Iimpawu ukubunjwa leengxaki

akukho ndawo apho ayikwazi ibonakala aplasia ebantwini. Le meko yezifo yomnye amalungu imazi ikwazi ibangela enye hypertrophy (aplasia omnye kwamadlala ezidalwe kungabangela hypertrophy zabanye). Ngoko ke, kukho indawo, imbuyekezo kwemisebenzi elahlekileyo.

Kudla akukho yinxalenye yomzimba, ezifana aplasia of the I-corpus okanye ingqondo ukuqgiba (imeko ekuthiwa arinentsefaliey), njl Aplasia ye inwebu ngoyena ngokuqhelekileyo ibonwa kwi entlonzeni. Kweli thuba usana ozelwe sisiphene elibhaqiweyo, apho ngokuqhelekileyo ayidluli-5 cm. Kodwa isimo odityanisiweyo enjalo, emi nzulu, umzekelo umthetho, izihlunu aplasia, kwimeko slits osandul layo lingatywinwanga (t. N. Dizarfiya).

Uphuhliso ezingahambi esiqwini bone

Njengoko kwezi meko zichazwe ngentla, aplasia ithambo ekwimo ekwanti inqabile kakhulu. Ngoko, xa isifo onjalo lomzimba lesiquluba nomonde asisifutshane iphuhlise equinovarus unyawo ukukhubazeka (edge ngaphambili kwi efanayo ixesha bayavuswa, kwaye engaphandle - ezishiyiweyo), lesiquluba egosogoso, akukho ithole kunye nezihlunu peroneal.

amatyala Aplasia ngabanye ezibhalwe zonyango amalungu omzimba, kudla ngokwenzeka kunye nemilenze yabantu. Oku kunokuba ukungabikho iminwe enye okanye ngaphezulu okanye sonke isandla okanye unyawo. ukunqongophala rhoqo lokukhethwa zengalo, bembande, igxalaba, umlenze, phambi unyawo okanye ngesandla.

Aplasia ngayo, yaba lukakayi, ingqondo

Xa aplasia yinqontsonqa yayo ngamathambo yokakayi, nto iyeza ikwabizwa ngokuba "ukakayi fenestrated", oko esekwe iziphene yokuba ubungakanani ezahlukeneyo nemilo. Kodwa periosteum (inwebu ezinezikhondo ukuyigubungela ithambo) kunye isikhumba kwindawo ezi iziphene ahlale. Bona ebekwe ubukhulu becala kwimimandla Parietal kunye ngokungqalileyo.

Ukuba nosana akukho amathambo lukakayi, oko kudla kunye nabo umongo aplasia (Ibizwa kwakhona anencephaly). Le ngezifo liyabulala 100%. Ngaphezu koko, 75% yabantwana nangoku kufa Esibelekweni, kwaye abanye bangabi ngaphezu kweentsuku ezi-5 emva kokuzalwa.

Nangona eyaziwa kwimeko yokuzalwa kwi US ngo 1992, intombazana unesifo onjalo, owayephila kweminyaka emi-2 kunye neentsuku 174. Zokuphefumla ukusebenza izibilini emzimbeni wayo lwaqhutywa yi esiqwini ebuchotsheni igcinwe. Kodwa ke, nangona kunjalo, intombazana ngamathuba athile idityaniswe baphefumla ngokunjalo iingxaki asakhasayo kukhokelela stop yayo.

Aplasia kwe wesibeleko kunye lobufazi

Amatyala yonomgogwana okanye ukungabikho isibeleko, tubes kunye lobufazi - ukungaqheleki akufane nazo. Abasetyhini abanalo, awukwazi kumitha okanye ukwenza umntwana wakho.

Ingxaki ibanjiwe idla sele phambili ekufikeleleni ukufikisa. Kugqirha Mfazi ukuba izikhalazo malunga yokunqongophala sexesheni kunye (xa kungekho lobufazi), nakwenzeka lobomi ngokwesini. Kulo mzekelo, isigulane kudla igcinwe isakhiwo umzimba eziqhelekileyo ze-kakuhle neempawu zesini eziziisekondari.

Ukuba isigulana umntu aplasia kwenxenye kwinxenye yelungu lobufazi, mhlawumbi akhalaze ukopha ngenyanga ngeempumlo, isisa ibele, kunye neentlungu zokuzoba esiswini asezantsi, ezo zihamba kunye nokwanda yokumpompoza sexesheni, ekubeni nencindi xa Uxilongo ayiyi kuba nagama.

Loo into kukhokelela iimanyano ithumba - babizwa ngokuba hematocolpos. Njengoko bekhula, eziqukayo asezantsi iintlungu esiswini abonakale zibukhali, kwaye xa suppuration efakwe ngokwemvula ubushushu, ukudala iimeko ezithandwa nokudumba. Isigulana kulo mzekelo ubonisa umsebenzi ongxamisekileyo.

Xa yamathumba ye isibeleko ayikho akukho ndlela, ekubeni akukho umzimba, ikhuphe igazi.

Aplasia - akukho kusoloko isigwebo sokufa

Le ukusebenza komzimba aplasia womntu ngamalungu ezahlukeneyo, iithishu okanye iindawo zomzimba eyahlukileyo. Ezinye iintlobo aplasia (engekho zifaka yobuchopho, imisipha intliziyo, izintso zombini, njalo njalo. N.) Ngaba akuvumelani ebomini. Abanye kunokubangela kwekhono komzimba, yaye akukho utyando iya kukhokelela ukufa isigulane (Ithemba diaphragmatic , okanye isifo Hirschsprung).

Kodwa ke ukungabikho inxalenye okanye yonke lomzimba, kwakunye aplasia le isibeleko, iyahambisana ebomini. A pair elinye lomzimba ongaphuhliswanga, ezifana aplasia ngomoya omnye kwezintso, hypertrophy maxa wambi babuyekezwe ngokupheleleyo komnye, yaye ngaloo ndlela unako ngokwezonyango ukuzibonakalisa ubomi yesigulane.

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