ZempiloDiseases and nemibandela

Angiomyolipoma sezintso: Ingaba oko kuyingozi ebomini, Ubangela, Iimpawu and Treatment

Njani na kidney angiomyolipoma, nokuba ezisongela ubomi? Le meko kuthetha ukubandakanyeka kukutyeba lwezidumbu kwinkqubo interlayer, tissue kwezihlunu, kunye epithelium sezintso. Xa ithumba ebubonisayo ngakumbi iqulathe okunamafutha.

Njengomgaqo, angiomyolipoma isasazwa ukuya kwizintso. Esi sifo kuchaphazela umntu na ubudala, kodwa xa abantu abadala kuqhelekile ngakumbi. Xa iqela ubungozi ibandakanya abantu ukusuka kwiminyaka engama-40 ukuya kuma-60. Kufuneka kuqatshelwe ukuba amatyala abhalwe rhoqo kwabasetyhini. Imbi kangakanani na esi sifo, kwaye ishenxisa angiomyolipoma sezintso? Treatment kunye nengozi ebangelwa sifo, kuya kuthi achazwe kweli nqaku. Xa eqalwe ngexesha unyango ngezifo lupheliswe ngokupheleleyo.

iintlobo zezifo

Angiomyolipoma - ithumba nabungozi kwi kwizintso. Esi sifo wasamkelayo elinye igama - "hamartoma kwezintso". Neoplasm ihlelwa ezimbi mesenchymal echaphazela kwizihlunu ezithambileyo.

iintlobo ezibalulekileyo ezimbini izifo: uhlobo manqapha izifo zamabanga yemfuza.

Kwimeko yokuqala, nethumba ichaphazela umzimba ngokwawo, ngaphandle ufuzo, yaye kwimeko yesibini, indima ekhokelayo idlalwa yofuzo.

Kukho kwakhona sisifo esahlukileyo ngokupheleleyo Bourneville-Pringle, okanye sclerosis ezinabileyo. Xa uthi umonakalo nezintso, kodwa ubonisa nezinye iimpawu.

Ukuba Ithumba yenzelwe ekhohlo okanye ekunene kidney bene sisilonda esidumbileyoesingaphakathi ngomoya omnye. Ukuba nemvelo olufunyanwa izintso zombini, oogqirha bathi malunga ifomu mazwe. uhlobo unilateral ikhula-75% yamatyala.

Ukongeza angiomyolipoma kunokuba ekuso ne Nedlac.

Xa uhlobo wendlela iqhuma kwi ngokuya iqulethe izihlunu imisipha, okanye amafutha emzimbeni, nto leyo yezonyango kuxhaphake kakhulu.

Xa uhlobo Nedlac kwithishyu adipose ayikho. Oku nzima unyango. Ngenxa okunamafutha inyama lwancothulwa sakugcina nomthelela. Kwakhona le fomu kunzima ukubona. Kulo mzekelo, amathuba imiyinge lobuxoki yamathumba ingozi kunye nangezilonda amabi.

Yintoni ngobambana kwi sifo?

Ngokuqhelekileyo, xa sifo kwinkqubo zophendlo lwezifo ezibandakanyekayo kunye neuron le sezintso. Ukudumba lula ukusekwa philisi, nto leyo sibiyelwe angabikho ephilile.

Yintoni nethala sifo efana angiomyolipoma sezintso (ekhohlo kunye nezintso ekunene) na? Kuyingozi kuba ngamanye amaxesha iqalisa meko ekhethekileyo. Oku kwenzeka ngaxeshanye kwizinto ezimbi, umz unyango okhethiweyo ngokungachanekanga okanye ubukho ezimbi ezongezelelweyo kwizintso.

Neoplasm uyakwazi sikhule le Vena cava kunguhata, kwiindawo nkovu zibekwe kufutshane okanye perirenal ntambo. Kwezinye iimeko, abantu abachaphazelekayo kunye negazi nempahla, nto leyo iintsuba, ukumqumbisa okuvela ukopha.

Abantu abaninzi bayazibuza ukuba yintoni na angiomyolipoma eyingozi? Sivame ukuxilongwa kinking nemithambo. Ngoko kukho Ukophuka Ukonakala onokubangela ukopha lwangaphakathi olukhulu, ephethe kusisisongelo kubomi umguli. Igazi engena kwisisu kwaye Ukuvalela kuyo. iindonga semithambo, eziqulathe izicwili kwezihlunu uba ubukhulu ujikajikeleza, awafuneki kwezihlunu lithuthwa ngokupheleleyo okanye ngokuyinxenye kungena nokuhlangana. Isiphumo kwaphawula perforation, leyo ezisongela kwemithambo kunye nezinye iingxaki eziyingozi.

Ezibangela isifo

Uphuhliso esi sifo ezinokubangelwa yezizathu ezahlukeneyo ngokupheleleyo.

Kuba eziliqela ukunisa ukuze ithathelwe ingqalelo:

  • Ukukhulelwa. Inkangeleko nethumba ixhomekeke kumanqanaba hormone. Njengoko sisazi, abasetyhini ngexesha yokumitha kwandisa inqanaba estrogen kunye dlala, nto leyo ibe negalelo kuphuhliso sifo.
  • Yentsusa yemfuza. Njengoko kukhankanyiwe ngasentla, le ezingaqhelekanga, kungenziwa phambi sifo Bourneville - Pringle. Esi sifo yemfuza. Izazinzulu ziye zafumanisa izakhi na ilifa.
  • Iindidi sifo iinkqubo nezintso, leyo kunye nezinye izinto, ukuze bandiqumbise kakuhle ithumba. Therapy, kule meko kubandakanya ukususwa zonke izifo ezihamba.
  • Ngokubonakala kwezinye neoplasms. Umzekelo, angiofibroma kuphuhliswa. Le ngezifo kuqhelekile kakhulu. Echazwe isifo inqaku iqalisa ukuphuhlisa phantsi kwempembelelo yayo.

symptomatology

kubonakala njani angiomyolipoma sezintso? I eyingozi ngakumbi esi sifo? Nokuphathwa ngexesha esi sifo enokwenziwa lupheliswe ngokupheleleyo. Kodwa isifo wengcibi lilele yokuba umlinganiswa wesinxibo kunxitywe ekuqaleni iimpawu ngezigaba. Obubonakala ezibonakalayo ngexesha ithumba lokuhlasela.

Kuba eziliqela iimpawu kufanele kuqwalaselwe:

  • Imvakalelo ubunzima ekhohlo okanye ekunene kidney, kwakunye ngasemva. Kuyaphela kungenzeka esisu sehlise umva. Ntlungu ukuba okuwisa, ezibuhlungu okanye ahlabayo. Bona lubonakala ngokuba ngamandla amakhulu ngexesha amathuba kunye nezinye iintshukumo. Oku kubangelwa hemorrhages zasekuhlaleni.
  • Yesi wegazi. Bayakwazi kwenzeke ngaphandle kwesizathu kwaye kaninzi ngokwaneleyo.
  • Le admixture negazi yokuchama.

Ukuba Ithumba ufumana ubungakanani enkulu, oko ukubonwa Ngokucofa.

Iziphumo sifo

Ukuba unyango zange yenziwe ngexesha elifanelekileyo, oko kusenokuba ineziphumo ezisongela ubomi yesigulane. Owokuqala ukwaphula iimpahla kunye nobukho ukopha kungenzeka peritonitis. Ndikunye yokopha lokugxininisa esisu kukho isoyikiso lokufa.

Yintoni kwakugcwele angiomyolipoma sezintso na? Nokuba siyabulala xa yokufumana ubungakanani enkulu? Kulo mzekelo, nethumba unako ukubeka uxinzelelo phezu amalungu ezikufutshane, ukuvimbela nokusebenza kwabo ngokupheleleyo. Umzekelo, kunye ngokoyiswa ekunene kidney na isihlomelo ukwazi, yaye isibindi. Neoplasm ukuze uqhekeko, naye oluvelisa isoyikiso kubomi babantu.

Enye ingxaki enkulu kukuba necrosis okanye bafe. Kulo mzekelo, izintso uyeke nje ukusebenza.

Musa ukulibala ukuba ithumba elihle nga zingaphumela ithumba.

ekuxilongweni

angiomyolipoma kwezintso (oonobangela, iimpawu, unyango ezo zichazwe kweli nqaku) kufuneka diagnosis ngexesha. Kuba unyango olusebenzayo kufuneka kwenziwe uphando olunzulu.

Eyokuqala kwenziwe uviwo ultrasound, nto leyo eya kunceda ukuchonga nethumba. Kwezinye iimeko, ekuqhubeni livakale magnetic umfanekiso kufanelekile.

ngezinga eliphezulu ucikizeko igazi nomchamo iimvavanyo jikelele. Uyakwazi ukubonisa imo kwenkqubo womchamo.

Kwakhona, kusetyenziswa indlela biopsy. Ngeenjongo zokucacisa uhlobo ithumba kidney sithathwa uhlalutyo ngu utyando ulwelo okanye okuhlatywa. Le ndlela yenza kube lula ukufumanisa ubukho bomhlaza.

Ukusetyenziswa kweziyobisi

Kukho ubungqina ngempumelelo ophezulu ezinye iziyobisi inhibitors kweli qela. Emva kwekhosi, unyaka eqhubekayo, kwezinye iimeko, nethumba ukuze zibhalwe ubungakanani ngesiqingatha.

Ukuba kukho ukwanda kakhulu angiomyolipoma, koko wabhenela kwendlela yotyando.

Ngokumalunga iindlela intsomi kunyango, oko kudla ayiniki ziphumo.

iindlela zokusebenza

Yenza kidney angiomyolipoma esisebenza, nokuba siyabulala xa kufuneka uqhaqho? Kwezinye iimeko, le kogrogriso kwaye ifuna nokususwa engxamisekileyo.

Ngokusekelwe kwiziphumo inkqubo yoxilongo lwezilwanya eziveliswe isicwangciso unyango ingcali ngamnye, nto leyo efunekayo ukuze bakuthathele ingqalelo izinto ezibalulekileyo njengoko iqonga apho uphuhliso ithumba, ubungakanani kunye nendawo.

Ngokuhambisana nemigangatho ngoku kwicandelo Oncology, ithumba, netoti engaphezulu kwe-4 cm, iyapheliswa ngokubamba buciko. Le ndlela isekelwe esweni ngamaxesha imeko yesigulane. Le isigulane eboniswe ubambe ultrasound kunye x-reyi diagnosis kanye ngonyaka.

ubukhulu Ithumba ngaphezu 4 cm kufuna unyango olukhulu.

Ngaphandle lingadluli ubukhulu kunongeno, inkomba ahlinzwe:

  • wavakalisa isifo iklinikhi ukuze inkqubela zesifo somhlaza;
  • ukwanda ngokukhawuleza nethumba;
  • phambi ukusilela kwezintso, nto leyo iba ezingapheliyo;
  • hematuria njalo.

Xa practice Oncology zokulamla kulindeleke ukusetyenziswa zoqhaqho obu buchule bulandelayo:

  • Resection kukho inxalenye ethile kidney, awalibethayo ithumba elihle. Olo tyando uyakwazi ukugcina umzimba.
  • Embolization. Kule ndlela, kwemithambo ebhalisele izixhobo ezikhethekileyo. Umthambo ondla AML. iindlela ezifana negalelo idlulela mithambo. Le ndlela isebenza yamalungiselelo kwinqanaba phambi uqhaqho. Kwiimeko ezinqabe kakhulu, embolization lisebenza njenge ndlela ezizimeleyo unyango.
  • Enucleation. Ngexesha lo msebenzi, ugqirha lususa ithumba ngaphandle umonakalo kwinyama sezintso ebumelwaneni.
  • Cryoablation. Ikwayindlela ezintsha ukuphelisa yamathumba ngenxa yeqabaka. Le ndlela zonyango isetyenziswa kuphela xa izixa ezikhulu ithumba.
  • nephrectomy Absolute buso. Xa isixa esikhulu nethumba ugqirha ugqiba ukususa ngokupheleleyo emzimbeni.
  • Laparoscopy. Le ndlela ibandakanya ukuphunyezwa eziliqela ukuhlatywa evumela ukuba angene kwigumbi kunye ezandleni yomzimba.

Outlook

Yenza angiomyolipoma eyingozi? amazinga abane nokusinda ukuba imeko iyathembisa. Ithumba fanele kudidi yamathumba nabungozi ise-philisi. Oku kuchaza ayaphumelela yonyango. Xa izigulane ezininzi, emva kotyando kukho bachache ngokupheleleyo.

isiphelo

Njani na angiomyolipoma kwezintso, nokuba bubomi, ukusongela, iye yachazwa kweli nqaku. Pathology ibhekisa kwinani kwezifo, kodwa bangenwe unyango. Lowo ephambili baphethwe ekwenzeni unyango oluchanekileyo.

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