An isifo samathambo yi purpura thrombocytopenic

Ngokuba lixesha lokuqala i samathambo purpura thrombocytopenic, kuchazwa 1735 Verlgofa ababona sifo kwiminyaka elishumi 'intombazana. Okwangoku phantsi le fomu gama ezidibeneyo samathambo thrombocytopenia, ukuba uyasilela autoaggression apho. Babonakala sophele diathesis kunye intswelo ekwanti of ziiplatelets. Bekela bucala ifomu acute kunye ezingapheliyo esi sifo.

oonobangela

purpura Acute thrombocytopenic ubunzima ngakumbi abantwana abaneminyaka emi-2 ukuya ku-9. purpura Thrombocytopenic kubantwana luphawulwa isiqalo ngesiquphe kunye ibuyambo ekhawulezileyo. Uphuhliso obubonakala onyango sivame ukukhuthaza igciwane lohlobo lwe iphecana eliphezulu zemiphunga okanye lokugaya. Ngowe-10% amatyala izifo ezinxulumene kunye nophuhliso varicella virus, yintsholongwane Epstein-Barr, ugonyo, BCG immunotherapy. Zegazi intshabalalo ngenxa impendulo omzimba eziphilayo kunokuba isenzo kwale ntsholongwane.

iintlobo Chronic of thrombocytopenia kuhlala ngaphezu kweenyanga ezi-6 kuthiwa purpura idiopathic thrombocytopenic. Unobangela sifo akaziwa. Thrombocytopenic purpura kaninzi iqala elivisayo, ukufikisa. Okunye kuxhaphakile kwabasetyhini.

obubonakala zonyango abonakale ngokuthe ngcembe. Luphawulwa ikhosi abanezifo qho okanye elide kweso sifo. isiseko Pathogenetic wezifo sikhulu kwaye nolukhawulezayo intshabalalo zegazi ngu autoantibodies nxamnye nawo.

picture clinical

Eluswini izigulane ezineempawu ze uhlobo ukopha microcirculatory njengoko punctate irhashalala petechial hematoma ezincinane ongama, purpura kwi isifo ngomlomo. Luphawulwa ukopha of kwiinwebu impumlo, iintsini. Utshintsho kwi eluswini badla zimi kumphezulu phambi weziphelo ibhuthi, engasentla nengasezantsi. ekumisweni legazi elikhulu kwiziza inaliti ungalindela. Maxa wambi kusenokubakho ukopha kungena sclera kunye retina, ukopha ukusuka lokugaya. Xa abafazi, kukho hemorrhages kwi zamaqanda. Xa iintlobo okunzima ukopha isifo sezintso esinokubakho.

purpura Thrombocytopenic kungakhokelela kubunzima eziyingozi ezifana Ukopha ebuchotsheni kunye legazi subarachnoid. Uphawu yi HIV cuff uvavanyo-Konchalovsky Umcinga-LEED: ukubunjwa hemorrhages kwiindawo eluswini ucinezelo. iindawo nkovu, isibindi kunye udakada ayikho banzi.

ekuxilongweni

Eyona iphambili kwelebhu kukunciphisa inani ziiplatelets. ke umthetho ixesha ekunqandeni igazi. LweeHedfowuni plasma kuye inyusiwe. Kwiimeko ezininzi, kumiselwa ukwanda kwe immunoglobulin G ziiplatelets. Emva ukopha ebalulekileyo ichaziwe etsolo ukopha anemia.

unyango

Ukuba unesifo thrombocytopenic purpura, izigulane eziqala unyango kunye corticosteroids. Ngexesha unyango, izigulane waphawula ukunyuka okuthe chu zegazi ubala ude kuxolelwe epheleleyo. Ukungabikho ukusebenza corticosteroids kunye immunomodulators emiselweyo delagil. Ngenxa kwawo unyango endala kwisithuba seenyanga ezi-6 isincomo enza splenectomy.

Enye indawo unyango - zolawulo amathamo ophezulu immunoglobulin ukuba isitofu efakwa iintsuku ezi-5. Ezi amalungiselelo okunqanda izilwa yekeyeke kwaye susa wentsholongwane egazini, iintsholongwane kunye namanye awakwazi.

Ngowe-80-90% lwezigulana kwakhona ezizenzekelayo lwenzeka kwisithuba seenyanga 1-4. Kwezinye iimeko, purpura thrombocytopenic elinokuthatha ukuya kuma kwiinyanga ezili-12. Isifo onesifo relapsing: ukopha amaxesha enye kunye nexesha kuxolelwa.