Zempilo, Diseases and nemibandela
Diathesis ukopha
Sophele diathesis - igama generic liqela izifo ezahlukeneyo, Simanywe osemqoka omnye - ukopha. Kukho zombini iintlobo sofuzo kwaye ziyafikelelwa. Apha umzekelo, izifo ezintathu ezahlukeneyo kweli qela.
Sophele vasculitis, ebizwa kwakhona ngamanye purpura izifo-uEnoki. Le diathesis ukopha ixhaphakileyo. Isizathu sokuba oku bubonakala ngezifo of izitshanguba microvascular non-ngqo, nto leyo ekhokelela ukopha kunye nophuhliso thrombosis. Ibangela zinto zibandakanya, ukusabela abandayo komzimba kunye nefuthe gazi. Kule sifo iindlela ezine:
- umbane;
- Isiqithi, elinokuthatha ukusuka kwiiveki eziliqela ukuya kwiinyanga ezimbalwa;
- zinde - ingahlala ukusuka kwiinyanga ezimbalwa ukuya kwiminyaka emininzi;
- relapsing, kunye ixesha elide ukuze kuxolelwe izinzile.
Iqale usoloko luphawulwa ifiva, ukususela imashumi mathathu anesibhozo - mathathu-kwehla yaye ngokuthe ngcembe nokunciphisa ukuba subfebrile. Ngaxeshanye, iqalisa ukuvela purpura, apho maxa wambi kukho izinto ezindlwini. Xa isifo kakhulu kwi Kumaziko izinto yabangxamayo kubonakale nakujoliso olutsha lwe necrosis, uze emva koko - brown. Emva kokuba zanyamalala yabangxamayo kwi nombala eluswini ngokuyimfuneko kuhlala kwiindawo eziza kuba ebonakalayo ixesha elide. Ngokuthe ngcembe, iintlungu kwamalunga amakhulu. Kwiimeko ezininzi, ingakumbi abantwana, iphuhlise mhlawumbi iintlungu ngokusisigxina okanye paroxysmal esiswini, nto leyo ibangelwa ukopha mesentery kwaye eludongeni emathunjini. Kubonakala ukugabha wamagazi. Zinokuchaphazeleka uhlobo glomerulonephritis kwezintso - nokuba bukhali okanye engapheliyo. Xa umchamo, ngokulandelelana, iiproteins kunye negazi ibonakala.
Uxilongo isekelwe kwikliniki isici. iimviwo Laboratory siqinisekisa zisasazwe intravascular coagulation syndrome.
Indlela ukuba ndiphilise diathesis-uEnoki purpura? Isigulane kufuneka esibhedlele ukuze linegunya, ukuphumla engqongqo ukhuko kufuneka babonwe kangangeeveki ezintathu ubuncinane. Ngenxa yokuba amachiza asetyenziswa lweeHedfowuni, ascorbic acid kunye rutin. Contraindicated iziyobisi sulfa, elwa ukuyifundisa. Akuvunyelwe ukuba asele ikofu, ikoko, amaqunube, citrus iziqhamo, naziphi iziselo iziqhamo kunye ayo. Kwimeko apho kukho intlungu ngokukhawuleza kwamalunga kusetyenziswa indomethacin, analgin Brufen.
Ngokokugqama i diathesis ezophayo, apho kungenxa yokusilela Factor VIII emzimbeni kunye factor inkqubo IX of igazi ekunqandeni. Esi sifo sibangelwa ezidluliselwa zemfuza kwi X chromosome, oko yenethiwekhi - umfazi kunye umntu agule. Ekubeni igazi uphelelwa ngamandla ayo ihlwili, isigulane afe evela nakuwuphi na ukopha. Kodwa ngaphandle opha amanxeba, ukopha ngaphantsi kwesikhumba inokuba izihlunu, em- namalungu ezinkulu.
Le diathesis sophele ezifumaneka ebuntwaneni. Kumnyinyiva loo nto ukunqanda ukopha ukusuka inxeba yosana. Umchamo ufumaneka hematuria.
Unyango igazi nomonde igazi okanye amayeza akhe, kwakunye Factor VIII mxube.
purpura thrombocytopenic Idiopathic, okanye isifo purpura thrombocytopenic. Okunye kuxhaphakile kwabasetyhini. Esi sifo esidityaniswe ukuncitshiswa kwenani zegazi egazini. Ngaloo nto ibangela ukopha. Isizathu sokuba esi sifo kakhulu ezibangelwa iingxaki kunye nezifo. Esi sifo sizibonakalisa ngokuthi sibe nokopha kakhulu eluswini, ngokufuthi localized apha emilenzeni kunye nesiqingatha phambi umzimba, kwakunye kwindawo of inaliti. uphawu esibulalayo ibonisa umngcipheko ukopha esengqondweni - owophayo kwi ingaphakathi amehlo okanye isikhumba. Iimpawu songe kunye nokulawula - HIV. Kukho ukwanda le udakada.
Uxilongo isekelwe kwiziphumo zonyango kunye elabhoratri.
Unyango lwenziwa prednisone ukuphumeza nempembelelo entle, wenza ukutofelwa zegazi abanikelayo kunye igazi elitsha.
Zonke ezi zifo zizigulane ezisongela ubomi, ingakumbi ukopha diathesis ebantwaneni.
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