Yintoni Morgagni-Stewart-Morel syndrome?

Syndrome of Morgagni-Stewart-Morel, imiboniso photo bunokubonwa kweli nqaku, kunqabile - abantu kwesigidi begula yonke enye kuphela elinamanci mane. Ngaphezu koko, xa kusenziwa, iingcali ubuso kakhulu kwi "ngamaqhekeza 'kwesi sifo, esi sifo kuba iphuhlisa wenzeka kangangeminyaka emininzi, yaye iimpawu ngezantya ezahlukeneyo. Izigulana kufuneka kuvavanywa na ugqirha phambi kokuba syndrome babonakaliswa ngokupheleleyo kwaye isigqibo uxilongo ngqo.

Le engaginyisi mathe ngayo esi sifo ifikelela, xa it yakha utshintsho ayibuyiseki umva zophendlo lwezifo emzimbeni. Emva koko, ukunceda isigulane cishe kungenakwenzeka.

indaba

Syndrome of Morgagni-Stewart-Morel kuye ngokupheleleyo esichazwe 1762, xa sezifo Italian Morgagni wavula isidumbu abafazi mane wafumana ukuqina ngaphakathi kwipleyiti ithambo ngokungqalileyo. Kwangaxeshanye, waphawula ukutyeba kunye ngokugqithiseleyo noboya obuninzi emzimbeni. Morgagni wafumana iimpawu ziyadlelana ichazwe ngokwenkcukacha imibono yakhe. Kamva, kwindibaniselwano iimpawu waphawula Morel and Stewart bakwazi ukongeza umfanekiso bezonyango ibonwa luvo nasengqondweni.

Yintoni isifo

Morgagni-Stewart-Morel syndrome - isifo apho ngokungqalileyo elibhaqiweyo hyperostosis ipleyiti ithambo yangaphakathi, nokutyeba kunye nenani kwezinye yonyango kunye metabolic ukuphazamiseka. Ngokugula uninzi kwenzeka kwabasetyhini, ubukhulu becala emva kweminyaka emashumi mane, kodwa ngamanye amaxesha ibonakale mathathu. Kuni yonke into eyindoda syndrome phantse lungenzeki, ngaphandle ezinqabileyo.

Umyalezo kunye Pathogenesis

Disease Morgagni-Stewart-Morel - syndrome, Pathogenesis kunye umyalezo apho kufuneka inkcazelo enye. Abanye ababhali bakholelwa ukuba kwezimilo nto yemfuza wadluliselwa ngokohlobo autosomal lubalaseleyo. Kukho izimvo ukuba syndrome ngokusondeleyo ezinxulumene ne-X-chromosome. Kwakukho iimeko xa isifo wabandezeleka izizukulwana zazine, ikakhulu abafazi.

Kukho iimeko ekwanti ukwenza izinto syndrome emadodeni. Kodwa manqapha, kwaye inzululwazi ayikenziwa kwaziwa njani esi sifo sisasazwa ngokusebenzisa umgca eyindoda. Abanye babekholelwa ukuba syndrome amaninzi kubonwa kwabasetyhini ngexesha ukuya exesheni. Kodwa data emfono ekuhambeni kwexesha, ukubeka le ngxelo ibe mbuzo.

Isifo kunokwenzeka ngenxa izifo (ubukhulu becala sinusitis), neuroinfections kunye ukwenzakala ebuchotsheni esibuhlungu. Wafunyanwa Morgagni-Stewart-Morel syndrome castrates abafazi abaye baba uqhaqho. Iinkalo ezithile syndrome ukuze emva unyango lomhlaza.

Kwakukho iimeko xa isifo zabonwa kwi izigulane:

• myoma wesizalo;
• zamaqanda sklerokistoz;
• galactorrhea ziqhu;
• infantilism zangasese.

Morgagni-Stewart-Morel syndrome: zokugula

Xa sifo nje ipleyiti ithambo ngokungqalileyo yangaphakathi ziyatyeba, kodwa maxa wambi ibhaqwe intloko hyperostosis kunye ebangwa-Occipital mmandla. Kukho utshintsho ezininzi obungabonakaliyo kwamadlala yonyango. Ukwandisa inani eosinophil kunye basophil iiseli. Qala kobubi adenomatous (lengqula, neuron adrenal kunye t. D.).

iimpawu

Xa umntu ufunyenwe Morgagni-Stewart-Morel syndrome, kukho eziliqela iimpawu okuluphawu ngayo:

• Izigulane uqala ukubona yintloko rhoqo.
• Ukutyeba, ingakumbi kummandla esiswini.
• Isikhumba igcina umbala oluqhelekileyo, kodwa ivele pyoderma nokulila nerhashalala.
• Kwiimeko ezininzi kukho hypertrichosis ngokukhawuleza.
• Esikhumbeni ebhalwe pastoznost baqale bandisa nemilenze, livela akrozianoz.
• Izihlunu buthathaka.
• Kukho utshintsho kwinkqubo sentliziyo amalungu zemiphunga (intliziyo nokwandisa imingcele, kukho iithowuni yokungeva ngeendlebe kunye nokungasebenzi kwentliziyo).
• Kuxhaphake ukuba ukujingxela, catarrh le iphecana eliphezulu bokuphefumla bronchopneumonia.
• Utshintsho kwi kwamadlala ezidalwe iimpawu iimpawu abanazo. Exchange usenokuba eqhelekileyo, ukwanda okanye ukuncipha.
• Ukwehla ukunyamezelana ekudleni. Amaxesha amaninzi seswekile kubonakala ngokucacileyo.

• Zaphazanyiswa sexesheni. Xa bekhulelwe, ngeli xesha imeko yesigulane kuguga.
• Kukho ukuphazamiseka Wayesoyika engqondweni. Bona azibonakali ngokohlobo lability ngokweemvakalelo, ukuba nochuku, efuna utyekelo kukudakumba.
• Internal plate ngokungqalileyo hyperostosis udla anquma amathambo ukhakhayi. Kwezinye iimeko, nkqu ukunyusa ubungakanani iinqwelo Turkish.

isifo

Morgagni-Stewart-Morel syndrome isinyathelo emzimbeni ngeendlela ezahlukeneyo. Rhoqo kuxhomekeke iqondo ukutyeba. Zicaca ibe nempembelelo enkulu kubomi:

• umsebenzi intliziyo kunzima;
• ngenxa ukuqokelelana amanqatha kwenzeka myocardium kunye pericardium;
• indawo ophezulu uvalo;
• kwegazi, yaye xa zidityaniswe ne yegazi kunye noxinzelelo lwegazi asakhulayo sisifo sentliziyo, nto leyo ibangele yokukhubazeka;
• ukuba isigulane kunye syndrome babe ngakumbi seswekile, ngoko iqala a disorder metabolic, nto leyo ekhokelela nje kuphela ukuhla ukusebenza, kodwa kunciphisa ixesha lobomi.

unyango

Ngaba lula ukuphelisa esi sifo ka Morgagni-Stewart-Morel? Unyango lwe sifo ubukhulu becala ukutya seswekile efanayo alinakunikezelwa kunye nokutyeba. Ukutya kufuneka kube elisezantsi-osidingayo, phezulu-protein, vitamin nezimbiwa iityuwa. Yokudla kunciphisa isixa carbohydrate kunye namafutha. Ukudla Baranov yabelwa ikakhulu.

Ukongeza, unyango yenziwa yokuthanjiswa awabelwa imithambo uqeqesho emzimbeni ukunciphisa buthathaka kwezihlunu nokuphucula ejikeleza neuropathy. Ukuba isigulana umntu ukungaphumeleli intliziyo, unyango onaso zabanjwa womchamo kardiopreparatami kunye t. D.