Zempilo, Amayeza
Kunjalo ke izifo abadala kunye nabantwana: oonobangela, iimpawu, unyango
Indima ibalulekileyo ukunyanga isifo enqabileyo kudlala diagnosis evumela ukuba ezohlula sifo evela kwinani nezinye izifo zempilo. unyango kunjalo kaThixo sifo elide, kodwa abantu abane lwezigulana ixesha ukubona oyingcali, kwiimeko ezininzi ezilungileyo.
Imbali sifo
Okokuqala afunda ngayo esi sifo 1897, enkosi ugqirha George Steele. Kodwa ngeli xesha sifo Sekunjalo ukuba oko kuqwalaselwa kuphela uhlobo isifo samathambo. Kuphela ngo-1971, Erik Bayuoters wapapasha izifundo ezahlula sifo evela kwinani iingxaki ezineempawu ezifanayo.
izibalo Medical zibonisa ukuba isifo ukugula onge ungakwazi ngokulinganayo abameli bazo zombini inkunzi nemazi. Noko ke, izigulane ezininzi wabhekisela kwagqirha iimpawu zesifo Sekunjalo waza wafumana isifo engqina - abantwana abangaphantsi kweminyaka eli-16 ubudala. Banikwa yobudala oselula onjalo, uninzi lwezigulane, uphethwe nzima kuba abazali kuqala waphawula iimpawu umntwana, kunzima ukukholelwa kubukho ezinjalo "ubudala" le ngxaki.
Izinto ezibangela izifo
Kude kube ngoku, esi umyalezo kwesifo engacacanga. izifundo ezininzi ezijolise ekuchongeni iinkalo esamcaphukisayo izifo kunjalo xa abantwana kunye nabantu abadala, ziye azaphumelela. Ngokutsho hypothesis eyamkelekileyo, esi sifo ngenxa yeziphumo emzimbeni okanye izifo egazini, kodwa ubungqina ukuxhasa le ngoluvo, akukho.
Oogqirha bazama ukuyamanisa sifo nokukhulelwa, ukusetyenziswa kwamayeza, kuquka zamadlala ababhinqileyo, uxinzelelo kunye nezinye izinto. Ngokutsho kweminye imithombo kunjalo ke sifo libhekisa ukuya kwizigulo sokuhlasela. Okwavela yangqineka kuphela ukuba kwisigaba ebonakalayo esi sifo luphawulwa utshintsho lwee- cytokines. Mhlawumbi iyeza elizayo uya kuba nako ukuchonga unobangela sifo, ngaloo ndlela ucazulule uxilongo kunye nokukhawulezisa ukukhula ngokutsha izigulane.
Iimpawu zesi sifo kunjalo kubantu abadala
Kunjalo kukho izifo, ogama iimpawu ezifanayo kwiqela nezinye izifo axilonge izinto ezininzi:
- Fever kwenzeka xa isifo Sekunjalo xa luphawulwa ifiva, sizalwa inani kwezifo ezosulelayo, inconstancy zabo. Ngokwemveli, iqondo lobushushu emini igcinwe kuluhlu oluqhelekileyo, kodwa kabini ngemini, nokunyuka ukuya degrees 39 nangaphezulu. Ngelo xesha elinye-sesihlanu izigulane hliswa kwezalathisi obushushu kunye nokuphucula kakuhle-ntle into anayenza yesigulane, nto leyo ebangela kubenzima kakhulu uxilongo.
- Xa kwincopho lobushushu umphakamo kwi isigulana babonakaliswa mlilo ulusu, thaca papules opinki okanye macula. Amaninzi, nerhashalala ibekwe esiqwini kunye eziphelweni proximal, ngaphantsi rhoqo - umfanekiso ubonisa kwamaqhakuvana ebusweni. Isinye kwisithathu kwezigulane yabangxamayo liphuma ngaphezu inshorensi lesikhumba, ezivela kwiinkalo ungquzulwano ucinezelo. Loo uphawu kuthiwa Koebner senzeko. Oku akusoloko kunye nerhashalala, ukurhawuzelela, kunye pink umbala wayo kakhulu kuba luthuthu kwaye wenze Ukunyamalala ngamaxesha kwizigulo imperceptible kumguli. Oogqirha yenza ukuxilongwa ze isigulane kufuneka phantsi kugqithise ubushushu, usebenze yimbonakaliso angawokubhuda. Kusenokuba ishawa efudumeleyo okanye ukuwiswa ngamalaphu ezishushu. kubonakaliswa Nedlac ze zesifo: alopecia, erythema nodosum, hemorrhages petechial. Kodwa practice, iimpawu ezinjalo zinqabile.
- Isigaba sokuqala lwesifo Sekunjalo bukaThixo luphawulwa imbonakalo myalgia kunye arthralgia. Kulo joint enye kuphela ngayo kuqala. Ekuhambeni kwexesha, esi sifo lugubungela namanye amalunga, ukuthatha uhlobo juvenile. Ubukhulu becala luchaphazela amalungu idolo, iqatha, iwotshi, hip, temporomandibular, metatarsophalangeal. Kodwa ke inkalo esi sifo, le nto eqhelekileyo ukuba isininzi amatyala, kukuba uphuhliso samathambo namalungu interphalangeal distal izandla. Le nto yenza ukuba umahluko izifo Sekunjalo ukusuka samathambo, lupus ebomvu okanye isifo samathambo.
- Ngowe-65% amatyala esi sifo lwenzeka kwi yangasemva lymphadenopathy. Isiqingatha izigulane anda kwiindawo nkovu wesibeleko. Kwangaxeshanye, kwezinye iimeko, necrotizing lymphadenitis kuthatha isimilo.
- Ekuqaleni esi sifo, izigulane ingxelo okuphawulekayo elivuthayo umqala, leyo kunaphakade.
- Kuba kunjalo ke sifo sizibonakalisa kunye Cardio-pulmonary kubonakaliswa njenge pneumonitis aseptic, tamponade kwentliziyo, threatened valvular lokubandezeleka yokuphefumla syndrome.
- Xa izigulane nokuphazamiseka ezimakishiweyo lwamehlo. Le cataract elukhuni, yamehlo kwenwebu lwendibanisela yamaqabane iridocyclitis leRibhon amehlo.
Kunjalo ke izifo ebantwaneni
Symptomatology zesi sifo abantwana eyahlukileyo kubantu abadala. Noko ke, ezabonakala kunjalo ke sifo abantwana lubricated, okukhokelela isifo kwalibaziseka kwaye unyango libaziseko. Ngamanye amaxesha samathambo ebuntwaneni ikhokelela nokukhubazeka. Ukuze uphephe oku, abazali kufuneka babe ingqalelo kakhulu imeko emzimbeni bomntwana. Kwaye xa iimpawu zokuqala wezifo zibhekisela lomntu ke onobu bugcisa abanezakhono. Wasungula ukuba kunjalo sifo ebantwaneni kunokubangela ukunyuka elibi kwi eziphelweni ezifuna ungenelelo yotyando.
lokufunyaniswa kwesifo
Ekubeni neze iimpawu ezithile zesi sifo, uphethwe nzima. Kwimeko nganye, ngolwamashumi iseyi sifo iphathwa njenge umkhuhlane wendalo ezingaziwayo. Kwezinye iimeko, le uphethwe "nokudumba". Kwaba kuphela emva kuthotho lweekhosi bangaphumelelanga unyango zintsholongwane kunye nenani ezongezelelweyo ngokuhlalutya oogqirha baye kwisigqibo ukuba sisifo omdala kunjalo ke. Treatment kunye nokuvuselelwa - ixesha unyango kunye ifuna kweliso unyango rhoqo. Kukwasebenza kwanjalo kuyo abantwana.
Xa kufunyaniswa isifo kwabhalwa iimpawu njengoko ifiva, ukudumba amalungu, ukwandisa ezalathelwe nkovu nasemqaleni nangokurhala, kunye nezinye izinto ezifunyenweyo ngokusebenzisa echocardiography, Itomography ayinakubalwa ultrasound. Olugunyazisiweyo kunye uvavanyo igazi ebonisa amanqanaba zegazi kunye iiseli ezimhlophe zegazi. sifo kwi kunjalo ukuze isigulane luphawulwa ukuncipha kwinqanaba iiseli ezibomvu zegazi. Xa izigulane abadala, C-izidubuli protein ephakamileyo kunye ferritin. Ngoko zePCR izilwa-anti-nuclear kwakunye factor samathambo idla negative.
Treatment ngexesha kuxolelwe
unyango Complex phased lwenziwa kwisigaba esebenzayo zesi sifo, okanye kuxolelwe. Kwimeko yokuqala, inkqubo lwenziwa esibhedlele, elinesibini - izigulane zifumana unyango kuyimfuneko, lo gama OPD okanye sanatoria kunye iiholide zempilo. Unyango kuquka amayeza, ukuyifundisa umthambo unyango kunye umyalezo.
Unyango ngexesha isifo oyingozi
Ngexesha izigulane exacerbation ukuthatha NSAIDs, immunosuppressants, glucocorticoids. Unyango usoloko elide. Le nto zombini kumguli nosapho lwakhe kufuneka Stock idosi enkulu nomonde. Kunjalo ke izifo abadala kunye nabantwana - kokugula kakhulu nokujongana kunokuba kuphela kwesifo ngexesha unyango emiselweyo ngokuchanekileyo.
Outlook
Emva unyango, iintlobo ezintathu kunokwenzeka kwesi sifo. Olungileyo kubo - recovery ezizenzekelayo waphawula kwesinye kwisithathu izigulane unesifo esinqabileyo. Enye esithathwini omnye izigulane kufuneka ifomu relapsing kwesi sifo ngamathuba athile. Eyona ndlela kakhulu nzima - sisifo esingapheliyo abantu abadala kunjalo ke. Unyango, ukubuyiselwa kunye nokuvuselelwa kule kunokwenzeka aziquki unyango yemveli kuphela, kodwa arthroplasty, uvumela ukubuyisela isifo joint kutshatyalaliswa.
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