Zempilo, Mayeza
I-Amyloidosis yeentso: iifom, iimpawu kunye nonyango
Kukho izifo ezininzi zesifo. Enye yazo i-amyloidosis, eyona ntlawulo ye-amyloid kwiifom. I-Amyloid yenziwe yimphazamiseko yokuxilonga kwaye iyinkimbinkimbi yeproteins kunye ne-polysaccharides. I-Amyloidosis yeentso zinamafomu ambalwa:
1. Iiprayimari (ebizwa ngokuba yi-idiopathic kunye ne-genyinogo amyloidosis), apho izizathu ezibonakalayo kunzima ukuzimisela.
2. Sekondari, eyenzeka ngokuchasene nemvelaphi yezifo ezingapheliyo.
3. I-Genetic (ifa, inzala), eyenzeka ngenxa yeengxaki ze-genetic zeprotheni synthesis.
4. Umdala
Njengokuba kukho umzekelo, i-amyloidosis yesibini yeentso ixhaphake kakhulu kuneyona nto ephambili. Kule meko, usulelo olubangele ukuvela kwalo luyahluka. Ingakwazi ukuphuhlisa ngenxa yesifo sofuba, i-osteomyelitis, kwakunye nezifo ezinxulumene nokuxhaswa kwemiphunga. Kwakhona le fomu yesifo ivela nge-rheumatoid arthritis, i-ulcerative colitis. Kwiimeko ezinqabileyo, i-amyloidosis yeentso zingenzeka ngaphandle kwesizinda se-sinusitis, i-tonsillitis, i-mastitis kunye ne-syphilis.
Njengomthetho, i-amyloidosis yeentso, iimpawu ezingabonakali, zinemiqondiso emininzi engundoqo:
1. Ukubonakala kobuqhophololo
2. Ubuthakathaka bexesha
3. Urhudo
4. Ukunyuswa kwengcinezelo yegazi
5. Ukungaphumeleli kwenkunzi
Ubukho beprotheni emcanjeni bubunjani bohlobo lwe-amyloidosis. I-Amyloidosis yeentso ikhokelela ekuphazamiseni intliziyo kunye nokungahambi kakuhle kwephepha lesisu. Njengomthetho, isigqi sengqondo esilungileyo silahlekile, kwaye ukuhluleka kwentliziyo kuyenzeka . Kukho ukunyuka kwesibindi kunye nesitebe, nangona iimpawu eziqhaqhayo zokuphulwa komsebenzi wazo zingabonakali.
Ukuze kuhlolwe i-amyloidosis yeentso, i-biopsy yeentso, isibindi, i-rectum kunye nekhumba kufuneka kwenziwe. Njengomgaqo, ukuqhuba i-biopsy yegobolondo ye-rectum kwi-70% yamatyala kunceda ukufumanisa i-amyloids. Oogqirha badla ngokuthembela kwiziphumo ze-biopsy.
Kwi-amyloidosis, i-echocardiography nayo iyenziwa, engabonakalisa izibonda zodonga lwe-ventricular udonga, i-septum phakathi kwama-ventricle, kunye nemiqondiso ye-diastolic engasebenzi. Ngokuqhelekileyo, kwesi sifo, igumbi le-ventricle langasese lesayizi eliqhelekileyo okanye elinciphileyo. Xa kwenziwa i-ultrasound, ubukhulu bezintso kwisi sifo bunokuqhelekileyo okanye bunyuke.
Amachiza anamhlanje akanalo unyango oluthile lwesifo esifana ne-amyloidosis yeentso. Utyando, oluqhelekileyo lisetyenziswe, lujoliswe ekupheliseni imbangela ebangela ukuphuhliswa kwesi sifo (oku kunjalo xa i-amyloidosis isibini). Njengomthetho, isigulane sinconywa ukutya okukhethekileyo kunye nekhosi ye chemotherapy. Ngamanye amaxesha i-hemodialysis kunye nokutshintshwa kweengtso zenziwa , ezithatha indawo yelichaphazelekayo.
Ukuba i-amyloids ikhona kwiphina iqela kwaye ayinasasazwa kuwo wonke umzimba, i-amyloidosis ayingozi kwimeko yesigulane. Izimpawu zesifo zichazwe kakuhle. Ngaphandle koko, ukubuyiswa kuxhomekeke kwonyango oluchanekileyo, ukunyameka kwonyango kunye nobukhulu besifo esabangela ukuphuhliswa kwe-amyloidosis.
Kukhuselekileyo ukukhusela ukuphuhliswa kwesi sifo. Njengomthetho, ukuthintela kuqulethwe kunyango olusifike ngexesha elinokubangela ukulimala kwezintso kunye ne-amyloidosis. Kule nto, kuyimfuneko ukuba uphononongo lweemviwo rhoqo kwaye uthathe iimvavanyo eziyimfuneko. Emva koko umngcipheko wokuhlaselwa kwaye ukuvela kwezilwanyana kuncitshiswa kakhulu.
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