ZempiloDiseases and nemibandela

Sokuwa kubantwana

Sokuwa kubantwana - sesinye sezifo zixhaphakileyo-luvo. Ebantwaneni, esi sifo kwenzeka ngo-3-4% yabo xa bebonke. Zokubonisa sokuwa, ALS, kunye neendlela zonyango kufuneka umahluko omkhulu. Kukho iintlobo ebubonisayo nesibuhlungu esi sifo. Eyokuqala yeyethu zabo kwaye musa ukuba unyango. Iifom elibulalayo kakhulu inkqubela lonke, kwaye unyango olungasebenziyo rhoqo. sokuwa kwabantwana abancinane picture lwezonyango Nedlac luphawulwa kukungabikho iimpawu ezicacileyo, yeyiphi ne utshintsho electroencephalogram.

Sokuwa kubantwana ithetha luphawu phindo, ukuxhuzula zabantu, isiseko apho isigxina yombane zemithambo-luvo esengqondweni, nto leyo luphawulwa nongqamaniso eliphezulu.

Ukwahlula inani elikhulu iintlobo zesi sifo. Xa uhlobo olwahlukileyo nqwelo zokungabikho sokuwa ebantwaneni, esibonakala ngekhondo kakhulu kwezonyango kunye nobunzima kakhulu.

Zonke ukuxhuzula uqale ukulahleka osezingqondweni, olwenzeka ngesiquphe, kwanokuqi- izihlunu skeletal lomzimba omzimba, ukubanjwa yokuphefumla, abafundi inimba. Oku kulandelwa hlaselo ngokuqhelekileyo uxhuzula indihlaziya-clonic kwimizuzwana engamashumi amathathu. Lubonakala yi twitching zesingqisho iingalo, imilenze, intamo, nentloko, ukubila gqitha, izinkcwe. Ngenxa ukuyekwa lokuphefumla umntu uba cyanotic (esiluhlaza). Maxa wambi kukho ulwimi ukuluma, ukuchama ngokuzenzekelayo. Total athole iintlobo zamashumi mane uxhuzula ebantwaneni abo uneempawu ezahlukeneyo lwezonyango, ALS, kunye neendlela zonyango. Nangona kunjalo, esi sifo zohlulwa ngokwendidi ezintathu: ngokubanzi (xa kuthe inkqubo ababandakanyekayo bobabini zifaka), ezesini (nokuhlutha luphumba iinxalenye ezithile ubuchopho), undifferentiated (zonke iindlela zale mihla diagnostic musa ukuvumela ukuba ukwabela ezi amatyala ezi ntlobo zimbini zokuqala).

Sokuwa kubantwana kufuna ukuxilongwa, kuba kuchaphazela impumelelo unyango, kwakunye liqikelele ikhondo elandelayo esi sifo. Ukuze uqinisekise sokuwa eyenziwa electroencephalography ingqondo, leyo ubhala iintlawulo zombane eziveliswa umzimba. Kwakhona yisa ezongezelelweyo - hyperventilation, photostimulation, ukulala nasekusweleni. Idla kuyimfuneko ukuphinda-test moshilongo oluchanekileyo (sokuwa kwiintsana). Ngokuphawulekayo kuphucula uxilongo EEG esweni ividiyo iquka ukurekhodwa ngaxeshanye electroencephalogram neevidiyo elibukhali kwisigulana. Lidla ngenxa elungileyo inika ikhompyutha kunye nemagnethi - livakale kwaye i engcolisayo Itomography.

Sokuwa kubantwana kusekelwe kumgaqo kuxolelwe iziyobisi ngcembe, nto leyo kwixesha elizayo kuya kukhatshwa ukurhoxiswa ngokuthe ngcembe iziyobisi. Ngenxa yoko, ukuncitshiswa iimpawu zonyango kuyaphunyezwa kwaye inika umgangatho wokuphila.

Izigaba ezingundoqo unyango lwesifo: Ubhaqo kunye isiphoso ebangela ukuxhuzula cupping izinto ingqondo, sizenza uxilongo ichanekileyo, ukukhethwa iziyobisi ezaneleyo unyango. Kuyimfuneko ukuba ukusombulula imbambano imfundo kunye nemiba yezentlalo. Eyona nto ibalulekileyo kukuba kukuchonga arhente ezenza ukuba unyango sokuwa. Ukuze ezi njongo, wasebenzisa iziyobisi antiepileptic, eziquka levitiratsetam, topiramate, tiagabine, felbamate, gabapentin, lamotrigine, oxacarbazepine, vigabatrin.

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