Zempilo, Diseases and nemibandela
Kidney polycystic
isifo sezintso Polycystic sisifo esibi kwaye kakhulu kunene, ngokuqhelekileyo inkqubo ndlela-ezimbini, kodwa ke kwizintso ukuze bahlukunyezwe shiyana. Isifo esibonakaliswa nonyebeleziso omabini amaqela cysts zezintso, ezo pouches ngeenxa kunye ulwelo zolwelo. Phantse njalo, isifo sezintso polycystic senzeka phambi yofuzo.
cysts Nesihlo ezinxulumene ngqo ne kukuvela ukuphazamiseka kwendlela tubules sezintso banoxanduva output umchamo. Ngenxa yoko, abanye babo ophela umane, ekhokelela ngokupheleleyo ulwelo yabo ekuvalweni, ngamanye umchamo. Ukusebenza oqhelekileyo, kidney, umchamo emva kokuba hit kwi tubules sezintso sithunyelwa bile yokuqokelela, yaye kubo ngokusebenzisa iindebe ezinkulu nezincinane of wezintso kwaye engena ureter ke ngoko kwazona ivela emzimbeni.
Ukwahlula iintlobo ezimbini eziphambili polycystic kidney ezahlukeneyo uhlobo ilifa. Ifomu yokuqala ixhaphake kakhulu ebuntwaneni, zambona umntwana, njengoko umthetho, ngoko nangoko emva kokuzalwa, wabiza autosomal polycystic sofuzo isifo sezintso, le yesibini kucala abaphakathi kweminyaka engama-35-40 kwaye kuthiwa autosomal lubalaseleyo isifo sezintso polycystic. uhlobo Autosomal evelele polycystic ihlangana njalo mmi sewaka umhlaba, yaye yenye ezivame izifo yemfuza. Kukho malunga 11-12 yezigidi. Abantu abanengxaki kwesi sifo. Ngowe-90% kwefom autosomal lubalaseleyo polycystic njengelifa kubazali, i-10% - isiphumo izakhi ezikhululekileyo.
Amaninzi, isifo sezintso polycystic banesifo abantu abaphakathi kweminyaka engamashumi amabini ukuya kumashumi amane. Isifo iphuhlisa ngokuthe ngcembe, phantse kwasesizalweni, ibangele inkathazo iqala kuphela nasebudaleni. Esi sifo sizalwa amadoda nabafazi ngokulinganayo, akunakwenzeka ukuchonga ayivalele naliphi na iqela labantu, ukubandezeleka ukusuka isifo ngaphezu kwabanye.
isifo sezintso polycystic: iimpawu.
Ngelishwa, owokuqala iimpawu zesifo sezintso polycystic kunzima ukuyidibanisa nesi sifo: uxinzelelo lwegazi oluphezulu, ukudinwa, iintlungu buthuntu kummandla empontshwa, ukuphazamiseka kwenkqubo sentliziyo, Ukuchama rhoqo, badla ugalelwe igazi. Iifom Advanced sikhatshwe yimbonakalo uPienaar polycystic esiswini. Amaxesha amaninzi ngokwaneleyo ukuba abe pyelonephritis ezinxulumene nesifo co, leyo kudala iimeko azivumi ukuba ukufuya kwamagciwane.
Kwimeko lomonakalo omkhulu ukuya parenchyma, izigulane zifumana ozaziyo lunxano kwaye umthamo omkhulu wamanzi, njengoko bachatshazelwe izintso polycystic akukho kuphinda nabakwaziyo ukuphulaphula ngokwaneleyo ukuchama. Isiphumo sale ukusilela na Ukuveliswa wayo yonke ulwelo.
Eyona ngozi inkulu uphuhliso polycystic isifo sezintso, apho izintso abakwazi ukuba nje ukuba yenze imisebenzi yabo.
isifo sezintso polycystic: unyango.
Ikakhulu unyango olucacileyo sifo lifinyele ukuze kunqandwe insufficiency ezinganyangekiyo kwezintso kunye nosuleleko yesibini izintso. Phambi iingxaki ezifana glomerunefrit elimisiweyo iihomoni steroid kwentamo kunye nobukho lwegazi - antihypertensives. Kwezinye iimeko unyango ngotyando kucetyiswa, nto leyo resection eyahlukileyo nemingxuma esinganyangekiyo olumele ekuphazamiseni ngomatshini umchamo lokuphuma nokukhuthaza ukonakala perfusion kwezintso. Ukongeza, izigulane kufuneka bakuphephe amandla ngokugqithiseleyo emzimbeni, behlunguzela, umgama omde, kufuneka uliqaphele imikhuhlane zosulelo, nokubeka iliso rhoqo imeko kwamazinyo kunye nomqala.
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